Definition/General

Introduction:
-Gastric hemangioma is a benign vascular tumor composed of proliferating endothelial cells
-It represents less than 1% of gastric tumors
-Most common vascular lesion of the stomach
-Can present as solitary or multiple lesions.
Origin:
-Arises from vascular endothelium of gastric wall
-May originate from submucosal vascular plexus
-Can involve multiple layers of gastric wall
-Represents hamartomatous proliferation rather than true neoplasm.
Classification:
-Capillary hemangioma (most common type)
-Cavernous hemangioma (large vascular spaces)
-Mixed type hemangioma
-Arteriovenous malformation (AVM) variant
-Pyogenic granuloma (reactive lesion).
Epidemiology:
-Can occur at any age but peak in 4th-5th decades
-Equal gender distribution
-Rare in children unlike cutaneous hemangiomas
-Sporadic occurrence in most cases.

Clinical Features

Presentation:
-Gastrointestinal bleeding (60-70% cases)
-Iron deficiency anemia from chronic blood loss
-Asymptomatic in small lesions
-Epigastric pain (20-30%)
-Hematemesis and melena in active bleeding.
Symptoms:
-Chronic GI bleeding leading to anemia
-Acute massive hemorrhage (rare)
-Postprandial discomfort
-Early satiety in large lesions
-Fatigue and weakness from anemia.
Risk Factors:
-Vascular malformation syndromes
-Hereditary hemorrhagic telangiectasia
-Blue rubber bleb nevus syndrome
-Klippel-Trenaunay syndrome
-Previous gastric trauma or surgery.
Screening:
-Upper endoscopy for GI bleeding
-CT angiography for vascular assessment
-MRI for lesion characterization
-Capsule endoscopy for small bowel involvement
-Genetic counseling for syndromic cases.

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Gross Description

Appearance:
-Red to purple polypoid or sessile lesions
-Soft, compressible consistency
-Well-demarcated from surrounding mucosa
-Multiple lesions possible
-Surface ulceration in bleeding cases.
Characteristics:
-Spongy texture with blood-filled spaces
-Easy bleeding on manipulation
-Variable size from few millimeters to several centimeters
-Blanching on pressure application.
Size Location:
-Size ranges from 0.5-5 cm (most <2 cm)
-Antrum most common location (40-50%)
-Body and fundus (30-40%)
-Multiple locations in syndromic cases.
Multifocality:
-Solitary lesions in sporadic cases (80-90%)
-Multiple lesions in Blue rubber bleb nevus syndrome
-Associated with cutaneous hemangiomas
-Small bowel involvement possible.

Microscopic Description

Histological Features:
-Proliferating endothelial cells lining vascular spaces
-Capillary type: Small, slit-like spaces
-Cavernous type: Large, dilated vascular channels
-Feeding vessels and draining veins identifiable.
Cellular Characteristics:
-Bland endothelial cells without atypia
-Single layer lining vascular spaces
-Minimal mitotic activity
-No cellular pleomorphism
-Pericytes around vessels.
Architectural Patterns:
-Lobular architecture in capillary type
-Large cavernous spaces in cavernous type
-Feeding artery and draining vein
-Smooth muscle walls in larger vessels.
Grading Criteria:
-Benign lesions by definition
-No malignant potential
-Absence of mitoses and atypia
-Well-formed vascular channels
-Endothelial cell monolayer.

Immunohistochemistry

Positive Markers:
-CD31 (95-100% positive)
-CD34 (90-95% positive)
-Factor VIII (80-90% positive)
-ERG (nuclear, 95% positive)
-FLI-1 (nuclear, 90% positive)
-Vimentin positive.
Negative Markers:
-Cytokeratins negative
-S-100 negative
-Desmin negative
-Smooth muscle actin (negative in endothelium)
-KIT negative
-GLUT-1 variable.
Diagnostic Utility:
-Endothelial markers confirm vascular nature
-CD31 and ERG most reliable
-Smooth muscle actin highlights vessel walls
-Ki-67 shows low proliferation (<5%)
-D2-40 may highlight lymphatics.
Molecular Subtypes:
-No established molecular subtypes
-GLUT-1 expression distinguishes from other vascular lesions
-WT1 positivity in some cases
-Prox-1 positive in lymphatic components.

Molecular/Genetic

Genetic Mutations:
-No consistent genetic alterations
-TEK mutations in some familial cases
-RASA1 mutations in capillary malformation-AVM
-PIK3CA mutations in some vascular malformations
-Somatic mosaicism possible.
Molecular Markers:
-Low proliferation index (Ki-67 <5%)
-VEGF expression variable
-Angiopoietin expression
-Tie-2 expression
-PDGF signaling components.
Prognostic Significance:
-Excellent prognosis with appropriate treatment
-No malignant potential
-Bleeding risk main concern
-Recurrence rare after complete excision.
Therapeutic Targets:
-Endoscopic therapy (sclerotherapy, band ligation)
-Surgical resection for large lesions
-Pharmacological: Beta-blockers, corticosteroids
-Interventional radiology: Embolization.

Differential Diagnosis

Similar Entities:
-Angiosarcoma (malignant vascular tumor)
-Kaposi sarcoma
-Pyogenic granuloma
-Arteriovenous malformation
-Glomus tumor
-Hemangioendothelioma.
Distinguishing Features:
-Hemangioma: Bland endothelium, no atypia
-Angiosarcoma: Atypical endothelium, mitoses
-Kaposi sarcoma: Spindle cells, HHV-8 positive
-Pyogenic granuloma: Reactive, ulcerated surface
-AVM: Direct arteriovenous connection.
Diagnostic Challenges:
-Distinguishing capillary hemangioma from pyogenic granuloma
-Separating from well-differentiated angiosarcoma
-Identifying syndromic associations
-Sampling artifacts from fragile tissue.
Rare Variants:
-Epithelioid hemangioma
-Spindle cell hemangioma
-Anastomosing hemangioma
-Microvenular hemangioma
-Targetoid hemosiderotic hemangioma.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen

[type], [size] cm

Diagnosis

[Capillary/Cavernous] hemangioma

Features

Benign vascular proliferation with [describe pattern]

IHC

CD31: +, ERG: +, Ki-67: <5%

Final Diagnosis

Gastric [type] hemangioma, [size] cm