Definition/General

Introduction:
-Pancreatic pseudocyst is a fluid collection without epithelial lining
-Develops as complication of acute pancreatitis
-Contains pancreatic enzymes and inflammatory debris
-Most common pancreatic cystic lesion
-FNAC shows characteristic paucicellular findings.
Origin:
-Results from pancreatic duct disruption following acute pancreatitis
-Enzymatic digestion creates cavity
-Fibrous wall formation occurs over time
-Contains pancreatic juice and inflammatory material
-No true epithelial lining present.
Classification:
-Acute pseudocyst (<4 weeks duration)
-Chronic pseudocyst (>4 weeks duration)
-Organized pseudocyst with thick wall
-Complicated pseudocyst (infected, hemorrhagic)
-Multiple pseudocysts possible.
Epidemiology:
-Complicates 10-15% of acute pancreatitis cases
-Male predominance (M:F = 3:1)
-Peak incidence 4th-5th decades
-Alcohol-related pancreatitis most common cause
-More common in developing countries.

Clinical Features

Presentation:
-Persistent abdominal pain after acute pancreatitis
-Palpable mass (large pseudocysts)
-Nausea and vomiting
-Early satiety
-Weight loss
-Biliary obstruction (head pseudocysts).
Symptoms:
-Epigastric pain (most common)
-Post-prandial fullness
-Nausea and vomiting
-Palpable abdominal mass
-Jaundice (ductal compression)
-Fever (if infected)
-Gastric outlet obstruction.
Risk Factors:
-Acute pancreatitis (any etiology)
-Alcohol abuse
-Gallstone pancreatitis
-Pancreatic trauma
-Previous pancreatic surgery
-Chronic pancreatitis.
Screening:
-CT scan (diagnostic imaging)
-MRI/MRCP for detailed evaluation
-EUS for cyst characteristics
-Serum amylase/lipase may be elevated
-Cyst fluid analysis confirmatory.

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Gross Description

Appearance:
-Unilocular cystic lesion without solid components
-Thick fibrous wall (mature pseudocyst)
-Contains turbid, brownish fluid
-No papillary projections
-Smooth internal surface.
Characteristics:
-Round to oval cystic lesion
-Thick fibrous capsule
-No epithelial lining
-Contains pancreatic juice
-Debris and inflammatory material
-May have calcifications in wall.
Size Location:
-Size ranges from 2-20 cm (average 6-8 cm)
-Body and tail most common locations (60%)
-Head involvement in 30%
-May involve peripancreatic tissues
-Lesser sac location common.
Multifocality:
-Multiple pseudocysts in 20-30% cases
-Usually related to severe acute pancreatitis
-May communicate with pancreatic duct
-Satellite pseudocysts around main lesion.

Microscopic Description

Histological Features:
-Fibrous wall without epithelial lining
-Chronic inflammatory infiltrate
-Granulation tissue formation
-Vascular proliferation
-Hemosiderin deposits
-Calcifications in chronic cases.
Cellular Characteristics:
-Fibroblasts and myofibroblasts predominant in wall
-Chronic inflammatory cells
-Macrophages with debris
-Endothelial proliferation
-No epithelial cells lining cavity.
Architectural Patterns:
-Cystic cavity lined by fibrous tissue
-Inflammatory granulation tissue
-Organized fibrous capsule
-Vascular ingrowth
-No true epithelial lining present.
Grading Criteria:
-Acute vs chronic based on wall maturation
-Complicated vs uncomplicated
-Organized vs unorganized
-Infected vs sterile
-Size-based classification.

Immunohistochemistry

Positive Markers:
-Smooth muscle actin (myofibroblasts in wall)
-CD68 (macrophages)
-Vimentin (fibroblasts)
-CD31/CD34 (vascular proliferation)
-Trichrome stain (fibrosis).
Negative Markers:
-Cytokeratins (no epithelial lining)
-CEA (helps exclude mucinous cysts)
-Chromogranin A (no neuroendocrine cells)
-Mucin stains negative.
Diagnostic Utility:
-Absence of epithelial markers confirms pseudocyst
-CEA levels in cyst fluid typically low (<192 ng/ml)
-Helps distinguish from mucinous neoplasms
-Inflammatory markers present.
Molecular Subtypes:
-No molecular subtypes recognized
-Inflammatory etiology determines characteristics
-Time-dependent changes in wall organization
-Associated with underlying pancreatitis type.

Molecular/Genetic

Genetic Mutations:
-No specific genetic mutations
-Reflects underlying pancreatitis etiology
-Inflammatory pathway activation
-Fibrosis-related gene expression
-No oncogenic mutations.
Molecular Markers:
-Inflammatory cytokines elevated in cyst fluid
-High amylase levels (>250 U/L)
-High lipase levels
-Protein content variable
-Low viscosity fluid.
Prognostic Significance:
-Size >6 cm less likely to resolve spontaneously
-Thick wall indicates chronicity
-Communication with duct affects resolution
-Location impacts complications.
Therapeutic Targets:
-Percutaneous drainage for large/symptomatic cysts
-Endoscopic drainage (transmural or transpapillary)
-Surgical drainage (cystoenterostomy)
-Conservative management for small asymptomatic cysts.

Differential Diagnosis

Similar Entities:
-Mucinous cystic neoplasm
-Intraductal papillary mucinous neoplasm (IPMN)
-Serous cystadenoma
-Cystic pancreatic neuroendocrine tumor
-Retention cyst.
Distinguishing Features:
-Pseudocyst: No epithelial lining
-Pseudocyst: High amylase/lipase
-Pseudocyst: History of pancreatitis
-MCN: Epithelial lining present
-MCN: Ovarian-type stroma
-IPMN: Ductal communication.
Diagnostic Challenges:
-Cystic degeneration of solid tumors
-Infected pseudocyst vs cystic neoplasm
-Sampling adequacy in FNAC
-May need cyst fluid analysis
-Clinical history crucial.
Rare Variants:
-Hemorrhagic pseudocyst
-Infected pseudocyst
-Pseudocyst with solid debris
-Multiloculated pseudocyst
-Extrapancreatic extension.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen Information

FNAC from pancreatic cystic lesion, [location]

Adequacy

Specimen is adequate for evaluation

Fluid Characteristics

[Volume] ml of [color/consistency] fluid obtained

Cellular Findings

Paucicellular specimen with [inflammatory cells/debris]

Epithelial Cells

No epithelial cells identified

Background

Background shows [proteinaceous debris/inflammatory cells]

Cyst Fluid Analysis

Amylase: [level] U/L, CEA: [level] ng/ml

Final Diagnosis

FNAC pancreatic cyst: Findings consistent with pseudocyst