Definition/General

Introduction:
-Placental chorioangioma is a benign vascular tumor arising from the primitive chorionic mesenchyme
-It is the most common non-trophoblastic tumor of the placenta
-Small chorioangiomas (<5 cm) are clinically insignificant
-Large tumors (>5 cm) may cause fetal complications
-The incidence is approximately 1% of placentas.
Origin:
-Arises from primitive angioblastic tissue in the placenta
-Represents a hamartomatous proliferation of capillaries
-May result from localized hypoxia
-Genetic factors may contribute
-Similar to capillary hemangiomas elsewhere.
Classification:
-Classified by histological pattern: Angiomatous type (mature vessels)
-Cellular type (immature capillaries)
-Degenerated type (hyalinized)
-By size: Small (<5 cm)
-Large (>5 cm)
-Giant (>10 cm).
Epidemiology:
-Incidence: 1% of placentas
-Small tumors: 0.5-1%
-Large tumors: 0.02-0.2%
-More common in multiple pregnancies
-Female predominance (2:1)
-Associated with advanced maternal age.

Clinical Features

Presentation:
-Small tumors: asymptomatic
-Large tumors: polyhydramnios
-Fetal anemia
-Congestive heart failure
-Hydrops fetalis
-IUGR
-Preterm labor.
Symptoms:
-Maternal symptoms: abdominal distension (polyhydramnios)
-Fetal symptoms: decreased movements
-Cardiotocography: abnormal patterns
-Growth restriction
-Preterm contractions.
Risk Factors:
-Advanced maternal age
-Multiple pregnancy
-Diabetes mellitus
-Previous chorioangioma
-Familial history (rare)
-High altitude residence.
Screening:
-Prenatal ultrasound: well-defined mass
-Doppler studies: high vascularity
-MRI for large tumors
-Fetal surveillance
-Amniotic fluid assessment
-Growth monitoring.

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Gross Description

Appearance:
-Well-circumscribed mass on fetal surface
-Dark red to purple color
-Soft, spongy consistency
-Pedunculated or sessile
-Lobulated surface
-Cut surface: honeycomb appearance.
Characteristics:
-Smooth capsule
-Rich vascular network visible
-Hemorrhage and thrombosis possible
-Calcification in older lesions
-Cystic degeneration may occur.
Size Location:
-Size: few mm to >15 cm
-Location: usually fetal surface
-May be subchorionic
-Cord insertion site involvement
-Rarely intraparenchymal.
Multifocality:
-Usually solitary
-Multiple tumors in 20% cases
-Bilateral distribution possible
-Associated with other placental abnormalities.

Microscopic Description

Histological Features:
-Proliferation of capillaries and small vessels
-Endothelial-lined spaces
-Surrounding stroma variable
-Immature mesenchymal tissue
-Mitotic activity low
-No cytological atypia.
Cellular Characteristics:
-Endothelial cells: plump, benign
-Pericytes present
-Smooth muscle cells in vessel walls
-Mesenchymal cells in stroma
-No malignant features.
Architectural Patterns:
-Angiomatous pattern: mature vessels
-Cellular pattern: solid sheets of cells
-Myxoid pattern: loose stroma
-Sclerotic pattern: fibrotic areas
-Combination patterns common.
Grading Criteria:
-Type I (angiomatous): mature vessels
-Type II (cellular): immature capillaries
-Type III (degenerated): fibrotic, calcified
-Vascular density assessment
-Maturation grade.

Immunohistochemistry

Positive Markers:
-CD31 (endothelial cells)
-CD34 (vascular marker)
-Factor VIII (endothelium)
-Smooth muscle actin (pericytes)
-GLUT-1 (vascular marker)
-Ki-67 (low proliferation).
Negative Markers:
-Cytokeratin (epithelial)
-S-100 (neural)
-Desmin (muscle)
-CD68 (macrophages)
-Trophoblast markers.
Diagnostic Utility:
-Confirms vascular nature
-Distinguishes from other tumors
-Assesses proliferation rate
-Rules out malignancy
-Guides management.
Molecular Subtypes:
-Capillary-type hemangioma
-Cavernous-type hemangioma
-Mixed-type lesion
-Sclerosed variant.

Molecular/Genetic

Genetic Mutations:
-VEGF pathway alterations
-Angiogenesis genes
-PDGF signaling
-FGF pathway
-Hypoxia-inducible factors.
Molecular Markers:
-VEGF overexpression
-PDGF-β expression
-FGF-2 upregulation
-Hypoxia markers
-Angiogenic factors.
Prognostic Significance:
-Size determines prognosis
-Large tumors: poor fetal outcome
-Small tumors: excellent prognosis
-Associated complications
-Recurrence rare.
Therapeutic Targets:
-Observation for small tumors
-Fetal surveillance
-Early delivery if complications
-Intrauterine interventions (selected cases)
-Postnatal surgery rarely needed.

Differential Diagnosis

Similar Entities:
-Teratoma
-Partial mole
-Placental mesenchymal dysplasia
-Arteriovenous malformation
-Subchorionic hematoma
-Chorangiosis.
Distinguishing Features:
-Chorioangioma: Benign vascular proliferation
-Well-circumscribed
-Teratoma: Multiple tissue types
-Immature elements
-Mole: Trophoblastic proliferation
-Vesicular change.
Diagnostic Challenges:
-Small lesions vs chorangiosis
-Degenerated tumors
-Calcified lesions
-Clinical correlation important
-Imaging correlation.
Rare Variants:
-Atypical chorioangioma
-Chorioangiomatosis
-Angiosarcoma (malignant)
-Hemangioendothelioma.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen Information

Placenta with chorioangioma measuring [X] cm

Diagnosis

Placental chorioangioma

Clinical History

[Polyhydramnios/fetal complications/incidental finding]

Gross Findings

Well-circumscribed [X] cm mass on fetal surface, dark red color

Microscopic Findings

Proliferation of capillaries and small vessels, benign endothelium

Tumor Characteristics

Size: [X] cm, Type: [angiomatous/cellular/degenerated]

Histological Type

[Angiomatous/Cellular/Mixed] type chorioangioma

Associated Complications

[None/Polyhydramnios/Fetal anemia/Other]

Prognosis

[Excellent/Good/Guarded] based on size and complications

Final Diagnosis

Placental chorioangioma, [X] cm, [type]