Overview

Definition:
-Breast milk jaundice is a benign, exaggerated form of physiological jaundice that occurs in breastfed infants after the first week of life, typically peaking around the second to third week
-Breastfeeding jaundice, also known as early-onset non-physiologic jaundice, is related to insufficient intake of breast milk in the first few days of life, leading to decreased bilirubin elimination.
Epidemiology:
-Breast milk jaundice affects approximately 10-30% of breastfed infants
-Breastfeeding jaundice is observed in 5-10% of exclusively breastfed newborns
-Both conditions are common and part of the differential diagnosis for neonatal hyperbilirubinemia.
Clinical Significance:
-Distinguishing between these two common causes of neonatal jaundice is crucial for appropriate management
-Misdiagnosis can lead to unnecessary interruption of breastfeeding, potentially impacting infant nutrition and maternal-infant bonding, or conversely, to delayed intervention in cases of severe hyperbilirubinemia.

Clinical Presentation

Symptoms:
-Breast milk jaundice: Infant appears well, gains weight appropriately, and has normal stooling and feeding
-Jaundice appears after the first 3-7 days of life and may persist for weeks to months
-Breastfeeding jaundice: Infant may show signs of poor feeding, lethargy, decreased urine output, and fewer bowel movements
-Jaundice appears within the first few days of life.
Signs:
-In both conditions, the primary sign is visible jaundice, progressing from head to toe
-In breastfeeding jaundice, dehydration may be evident
-Examination of the infant in breast milk jaundice is otherwise unremarkable, with normal feeding and growth
-Laboratory findings would show elevated unconjugated bilirubin.
Diagnostic Criteria:
-Breast milk jaundice is a diagnosis of exclusion
-criteria include: onset after 7 days of age, exclusively breastfed infant, otherwise healthy infant, exclusion of other causes of hyperbilirubinemia, and a decrease in bilirubin levels upon temporary interruption of breastfeeding or use of donor milk.

Diagnostic Approach

History Taking:
-Key history points include: type of feeding (breast vs
-formula), frequency and duration of feeds, quality of latch, infant's urine output and stool frequency, infant's activity level, and presence of maternal medical conditions
-Family history of jaundice is also important
-Rule out hemolysis, sepsis, and inborn errors of metabolism.
Physical Examination:
-Assess for signs of dehydration (mucous membranes, skin turgor, fontanelle), presence of hepatosplenomegaly, signs of infection (fever, lethargy), and extent of jaundice using the Kramer scale
-Thorough examination to rule out other causes of jaundice.
Investigations:
-Total and direct bilirubin levels are essential
-Unconjugated hyperbilirubinemia is typical for both
-Complete blood count (CBC) with differential to rule out infection
-Blood group of mother and infant, and Coombs test if hemolysis is suspected
-Reticulocyte count, peripheral smear, and direct antiglobulin test (DAT) for hemolytic causes
-Liver function tests (LFTs) if cholestasis is suspected
-Consider G6PD deficiency screening in endemic areas.
Differential Diagnosis:
-Conditions to consider include: physiological jaundice, breastfeeding jaundice (if breast milk jaundice is suspected), hemolytic disease of the newborn (ABO or Rh incompatibility, G6PD deficiency), sepsis, hypothyroidism, Crigler-Najjar syndrome (types I and II), Gilbert's syndrome, and breast milk *induced* cholestasis (rare)
-Breast milk jaundice is characterized by prolonged unconjugated hyperbilirubinemia in an otherwise healthy, well-fed infant.

Management

Initial Management:
-For suspected breastfeeding jaundice, the primary step is to optimize breastfeeding
-Increase feeding frequency to 8-12 times per day, ensure a good latch, and monitor weight gain and urine/stool output
-For breast milk jaundice, continued breastfeeding is generally recommended, with close monitoring of bilirubin levels.
Medical Management:
-Phototherapy is indicated if bilirubin levels exceed established thresholds based on age and weight, following AAP guidelines
-For severe hyperbilirubinemia unresponsive to phototherapy or as an adjunct, exchange transfusion may be considered
-If breastfeeding jaundice is severe and leads to dehydration, temporary supplementation may be needed, but the goal is to re-establish exclusive breastfeeding.
Surgical Management:
-Surgical interventions are not indicated for breast milk jaundice or breastfeeding jaundice
-These are medical conditions managed non-surgically.
Supportive Care:
-Ensure adequate hydration and nutrition
-Monitor infant's weight, feeding pattern, and elimination
-Educate parents on signs of worsening jaundice and when to seek medical attention
-Close follow-up with pediatrician or neonatologist is crucial
-For breast milk jaundice, reassurance and continued breastfeeding are key
-For breastfeeding jaundice, support and education on infant feeding are paramount.

Complications

Early Complications:
-The main risk associated with both conditions, if untreated or mismanaged, is severe hyperbilirubinemia
-In breastfeeding jaundice, dehydration and poor weight gain are early concerns
-In severe cases of hyperbilirubinemia, the risk of kernicterus (bilirubin encephalopathy) exists, though it is rare in breast milk jaundice due to its typically benign nature.
Late Complications:
-Kernicterus can lead to long-term neurological sequelae including athetoid cerebral palsy, hearing loss, and gaze abnormalities
-Inadequate feeding in breastfeeding jaundice can lead to failure to thrive.
Prevention Strategies:
-For breastfeeding jaundice, early and frequent breastfeeding, proper latch technique, and prompt identification of feeding difficulties are crucial
-For breast milk jaundice, education of parents about the condition and reassurance are key preventive strategies against unnecessary interventions
-Close monitoring of infants by healthcare providers is essential.

Prognosis

Factors Affecting Prognosis:
-Prognosis is generally excellent for both conditions with appropriate management
-Factors influencing prognosis include the peak bilirubin level, the duration of hyperbilirubinemia, the promptness of intervention, and the absence of underlying hemolytic causes or significant dehydration.
Outcomes:
-Breast milk jaundice typically resolves spontaneously over several weeks to months with continued breastfeeding
-Breastfeeding jaundice resolves once feeding is optimized and adequate milk intake is established
-Long-term neurodevelopmental outcomes are excellent when severe hyperbilirubinemia is prevented.
Follow Up:
-Infants with breastfeeding jaundice require close follow-up to ensure adequate weight gain and resolution of jaundice
-Infants with breast milk jaundice may require periodic bilirubin monitoring until levels normalize, but otherwise have normal follow-up for their age
-Parents should be instructed to monitor for any concerning symptoms.

Key Points

Exam Focus:
-Understand the temporal difference in onset: Breastfeeding jaundice is early (days 2-4), breast milk jaundice is later (after day 7)
-Breastfeeding jaundice is due to insufficient intake
-breast milk jaundice is due to factors in the milk inhibiting bilirubin conjugation
-Both predominantly cause unconjugated hyperbilirubinemia.
Clinical Pearls:
-Always reassess feeding adequacy in any breastfed infant with jaundice after day 3
-A trial interruption of breastfeeding can help differentiate breast milk jaundice
-observe bilirubin drop
-Reassure mothers that breast milk jaundice is not a reason to stop breastfeeding
-Phototherapy thresholds are critical for NEET SS and DNB exams.
Common Mistakes:
-Stopping breastfeeding prematurely for breast milk jaundice without confirmation
-Failing to adequately assess feeding and hydration in infants with breastfeeding jaundice
-Over-reliance on bilirubin levels without considering the infant's clinical status and feeding pattern
-Not considering other causes of prolonged jaundice in the differential diagnosis.