Overview

Definition:
-Constipation in children is defined as infrequent stools, hard stools, painful defecation, or fecal incontinence (encopresis) that occurs at least once a week for at least one month, in the absence of organic disease
-Functional constipation is the most common type, accounting for over 90% of cases.
Epidemiology:
-Affects 3-5% of children in primary care settings and up to 30% of those seen by pediatric gastroenterologists
-It is more common in toddlers and preschoolers during toilet training
-Boys and girls are affected equally.
Clinical Significance:
-Chronic constipation can lead to significant distress for the child and family, impacting school attendance, social interactions, and self-esteem
-Untreated, it can result in painful defecation, stool withholding, fecal impaction, overflow incontinence (encopresis), and urinary tract infections due to bladder compression by a fecal-loaded rectum.

Clinical Presentation

Symptoms:
-Infrequent bowel movements, defined as fewer than 3 stools per week
-Passage of hard, dry, or large stools
-Straining or pain during defecation
-Fecal soiling or leakage (encopresis), often misinterpreted as diarrhea
-Abdominal pain, usually in the left lower quadrant
-Decreased appetite
-Nausea
-Intermittent vomiting
-Passing small amounts of liquid stool around a fecal impaction (overflow incontinence)
-Stool withholding behaviors, such as posturing or tensing muscles.
Signs:
-Palpable fecal mass in the abdomen, particularly the left lower quadrant
-Dilated rectum filled with hard stool on digital rectal examination
-Perianal fissures or skin irritation from soiling
-Abdominal distension
-Poor weight gain in some cases.
Diagnostic Criteria:
-Rome IV criteria for functional constipation in children: At least two of the following, occurring at least once per week for at least one month: Two or fewer defecations per week
-At least one episode of fecal incontinence per week
-History of retentive posturing
-History of painful or hard bowel movements
-Large fecal mass in the rectum
-History of large-volume stools that may obstruct the toilet
-Diagnosis is typically made based on history and physical examination, excluding alarm symptoms suggestive of organic disease.

Diagnostic Approach

History Taking:
-Detailed birth history, feeding history, and toilet training history
-Onset and duration of constipation
-Stool frequency, consistency (e.g., Bristol Stool Scale), and associated pain
-Presence of abdominal pain, nausea, vomiting, or decreased appetite
-Fecal incontinence (encopresis) – pattern, frequency, and relation to defecation
-Stool withholding behaviors
-Dietary assessment: fiber intake, fluid intake
-Family history of gastrointestinal disorders or constipation
-Review of systems to identify alarm symptoms (see red flags)
-Red flags: Bilious vomiting, failure to thrive, bloody stools, fever, severe abdominal distension, anal stenosis, absent anal reflex, neurological deficits, or onset of constipation after 4-6 weeks of life.
Physical Examination:
-General assessment: growth parameters (weight, height, BMI), signs of dehydration or chronic illness
-Abdominal examination: inspection for distension, palpation for tenderness or fecal masses, auscultation for bowel sounds
-Rectal examination: assessment of anal tone, presence of fissures, palpation of rectal vault for fecal impaction, and consistency of stool
-Neurological examination: assessment of lower extremity reflexes, sensation, and sacral dimple/tuft of hair to rule out spinal dysraphism.
Investigations:
-In most cases of suspected functional constipation, investigations are not required if alarm symptoms are absent
-If alarm symptoms are present or if there is suspicion of organic causes: Abdominal X-ray: may show significant fecal loading but is not essential for diagnosis of functional constipation
-Consider for suspected impaction or intussusception
-Blood tests: Complete blood count (CBC) for anemia (e.g., iron deficiency), electrolytes, calcium, thyroid function tests if hypothyroidism is suspected
-Urinalysis and urine culture: to rule out urinary tract infection, which can be associated with constipation
-Swallowing study or gastrointestinal imaging: if dysphagia or other swallowing abnormalities are suspected
-Spinal MRI: if neurological deficits or suspicion of spinal cord abnormalities (e.g., tethered cord).
Differential Diagnosis:
-Hirschsprung disease: characterized by absence of ganglion cells in the distal colon, leading to functional obstruction
-Symptoms include delayed meconium passage, abdominal distension, and failure to thrive
-Celiac disease: can present with constipation or diarrhea, abdominal pain, and failure to thrive
-Hypothyroidism: can cause generalized slowing of gut motility
-Anal fissures: painful defecation can lead to stool withholding
-Irritable bowel syndrome (IBS): diagnosis of exclusion in children over 4 years, with recurrent abdominal pain associated with changes in bowel habits
-Neurological disorders: spinal cord abnormalities, cerebral palsy, autonomic neuropathy
-Metabolic disorders: hypercalcemia, hypokalemia.

Management

Initial Management:
-The cornerstone of management is a multi-faceted approach including education, disimpaction (if present), a regular bowel regimen, dietary modifications, and toilet training
-Education for child and family is crucial, explaining that constipation is common, treatable, and not the child's fault
-Reassurance is vital to reduce anxiety associated with defecation.
Medical Management:
-Disimpaction: If fecal impaction is present, it must be cleared first
-This can be achieved with oral osmotic laxatives (e.g., Polyethylene Glycol 3350 - PEG 3350, dosed higher, e.g., 1.5 g/kg/day divided doses for 3-4 days, or until impaction is cleared), or with rectal therapies (e.g., enemas or suppositories) under medical supervision
-Maintenance therapy: Once disimpacted, a daily bowel regimen is initiated to prevent reaccumulation of stool
-Osmotic laxatives are preferred for long-term use due to their safety and efficacy
-Common options include PEG 3350 (e.g., 0.5-1 g/kg/day, max 17-34 g/day, titrated to soft stools 1-2 times/day) or Lactulose (0.5-1 mL/kg/day, max 10-20 mL/day)
-Stimulant laxatives (e.g., Senna, Bisacodyl) should be used judiciously and for short durations due to risk of dependence
-Stool softeners like Docusate sodium are less effective for functional constipation
-Dietary modifications: Encourage increased intake of fiber-rich foods (fruits, vegetables, whole grains) and adequate fluid intake (water).
Toilet Training:
-Once a regular bowel pattern is established with medication, toilet training can begin
-Establish a regular time for sitting on the toilet (e.g., 10-15 minutes after meals), especially after breakfast, to take advantage of the gastrocolic reflex
-Use a child-sized toilet seat or a potty chair
-Ensure the child's feet are supported to allow for comfortable positioning and relaxation
-Encourage a relaxed posture (e.g., leaning forward with elbows on knees)
-Praise and reward efforts and success, avoiding punishment for accidents
-Stool withholding behaviors should be addressed with positive reinforcement and patience.
Supportive Care:
-Behavioral interventions are crucial
-Regular toileting schedule
-Positive reinforcement and sticker charts for successful toileting
-Parental education and support to manage anxiety and frustration
-Management of encopresis: Initially, disimpaction and a maintenance laxative regimen are essential
-Once stools are soft and regular, focus on consistent toileting
-Accidents should be managed calmly
-Biofeedback therapy can be considered for older children with severe encopresis and dyssynergia of pelvic floor muscles, though it is less commonly used in routine pediatric practice in India.

Complications

Early Complications:
-Fecal impaction: Failure to treat initial constipation can lead to severe fecal loading
-Overflow incontinence (encopresis): Liquid stool leaks around the impacted mass, soiling underwear
-Anal fissures: Painful tears in the anal mucosa from hard stools
-Urinary tract infections: Due to rectal distension compressing the bladder and urinary tract
-Abdominal pain and distension
-Nausea and vomiting.
Late Complications:
-Chronic functional constipation: If not managed appropriately, it can persist into adolescence and adulthood
-Behavioral issues: Shame, anxiety, social isolation, school avoidance due to encopresis
-Reduced quality of life for child and family
-Potential for psychological distress.
Prevention Strategies:
-Early recognition and management of constipation
-Adequate fiber and fluid intake from infancy
-Timely and positive toilet training experiences
-Prompt treatment of any anal fissures or pain associated with defecation
-Regular follow-up to ensure adherence to medication and behavioral strategies.

Prognosis

Factors Affecting Prognosis:
-Early diagnosis and consistent management
-Parental adherence to treatment recommendations
-Child's cooperation and engagement
-Absence of underlying organic disease or significant neurological impairment
-Effective management of stool withholding behaviors.
Outcomes:
-With appropriate and consistent management, the prognosis for functional constipation in children is generally excellent
-Most children respond well to laxatives and behavioral interventions, achieving regular, soft stools and resolving encopresis
-However, relapse can occur if treatment is discontinued prematurely or if lifestyle factors (diet, fluids) are not maintained.
Follow Up:
-Regular follow-up with a pediatrician or pediatric gastroenterologist is important, especially in the initial months of treatment
-The duration of treatment varies but often requires several months to a year or more, with gradual tapering of medication as bowel function normalizes and toileting habits are established
-Long-term follow-up may be needed for children with complex cases or those at risk of relapse
-Emphasis should be on empowering the child and family to manage bowel health independently.

Key Points

Exam Focus:
-Remember the Rome IV criteria for functional constipation in children
-Always rule out alarm symptoms before diagnosing functional constipation
-Disimpaction is the first step in managing significant impaction
-Osmotic laxatives (PEG 3350) are the first-line agents for maintenance therapy
-Toilet training should commence after disimpaction and establishment of a regular bowel regimen
-Encopresis is overflow incontinence, not true diarrhea.
Clinical Pearls:
-Educate parents that constipation is not a willful act by the child
-Use the Bristol Stool Scale for consistent communication about stool consistency
-Encourage children to sit on the toilet for 10-15 minutes after meals, especially breakfast, to harness the gastrocolic reflex
-Positive reinforcement is key for toilet training success
-Gradual tapering of laxatives is crucial to prevent relapse.
Common Mistakes:
-Starting stimulant laxatives as first-line treatment
-Discontinuing laxatives too soon without establishing regular toileting habits
-Punishing children for encopresis or accidents, which exacerbates stool withholding
-Failing to adequately disimpact fecal masses before initiating maintenance therapy
-Not thoroughly assessing for alarm symptoms, leading to delayed diagnosis of organic causes.