Overview

Definition:
-Developmental Dysplasia of the Hip (DDH) is a spectrum of abnormalities in the acetabulum and femoral head, leading to instability and potential dislocation
-It encompasses conditions ranging from acetabular dysplasia to complete dislocation of the hip joint.
Epidemiology:
-DDH affects approximately 1-3 per 1000 live births in Caucasian populations, with a higher incidence in females (5:1 ratio)
-Risk factors include breech presentation, oligohydramnios, firstborn status, family history of DDH, and certain genetic syndromes (e.g., Ehlers-Danlos, Down syndrome).
Clinical Significance:
-Early diagnosis and treatment of DDH are crucial to prevent long-term sequelae such as avascular necrosis of the femoral head, osteoarthritis, limp, and chronic pain
-Effective screening and management can lead to excellent functional outcomes.

Clinical Presentation

Symptoms:
-In infants, symptoms may not be apparent
-Parents may report asymmetry in leg length or thigh creases
-Older children may present with a limp, waddling gait, or pain in the hip or knee.
Signs:
-Key physical examination findings in infants include: Asymmetrical thigh folds
-Unequal gluteal folds
-Unequal knee heights (Allis sign)
-Limited hip abduction (especially in flexion)
-Positive Barlow's sign (for instability)
-Positive Ortolani's sign (for reduction of a dislocated hip)
-In older children, signs may include a Trendelenburg gait and pain on palpation of the hip.
Diagnostic Criteria:
-There are no strict numerical diagnostic criteria for DDH
-diagnosis relies on a combination of clinical suspicion, physical examination findings, and imaging
-Pavlik harness is indicated for stable hips with >20 degrees of dysplasia or unstable hips in infants <6 months
-Surgical intervention is considered for older infants or failed conservative management.

Diagnostic Approach

History Taking:
-Key history points to elicit include: Gestational history (breech presentation, oligohydramnios)
-Birth history (assisted delivery, prematurity)
-Family history of DDH or hip problems
-Previous assessment of hip stability
-Presence of genetic syndromes
-Any parental concerns about asymmetry or gait.
Physical Examination:
-A systematic physical examination of the infant hip is essential
-This includes: Assessing hip range of motion, particularly abduction in flexion
-Performing the Barlow and Ortolani maneuvers
-Checking for leg length discrepancy (Galeazzi sign)
-Observing gait if the child is ambulant
-Examining the spine for associated anomalies.
Investigations:
-For infants up to 6 months, ultrasound of the hip is the investigation of choice
-It assesses the relationship between the femoral head and acetabulum, and the Graf classification helps quantify dysplasia
-For infants older than 6 months or when ultrasound is equivocal, a plain radiograph of the pelvis (AP and frog-leg lateral views) is used
-Key radiographic measurements include the acetabular index, Shenton's line, and the center-edge angle
-Magnetic Resonance Imaging (MRI) may be used in select cases.
Differential Diagnosis:
-Conditions to consider in the differential diagnosis of DDH include: Transient synovitis of the hip
-Septic arthritis of the hip
-Legg-Calvé-Perthes disease
-Slipped capital femoral epiphysis (in older children)
-Femoral nerve palsy
-Neuromuscular conditions causing hip instability
-Contractures or spasticity leading to apparent asymmetry.

Management

Initial Management:
-In neonates and infants with suspected DDH, the initial management is based on the age of the infant and the severity of dysplasia
-For infants under 6 months with unstable hips or significant dysplasia, the Pavlik harness is the mainstay of treatment
-Proper application and regular follow-up are critical.
Medical Management:
-Medical management is primarily conservative, focusing on maintaining the hip in a reduced position to promote normal development
-The Pavlik harness is a dynamic brace that maintains flexion and abduction, allowing for controlled movement
-Continuous wear, typically for 6-12 weeks, is usually required.
Surgical Management:
-Surgical management is indicated for DDH that is irreducible, neglected, or has failed conservative treatment
-Options include: Closed reduction with spica casting (for younger infants)
-Open reduction of the hip (if closed reduction fails or if there are significant soft tissue contractures)
-Pelvic osteotomy (e.g., Pemberton, Salter, Dega) to improve acetabular coverage
-Femoral osteotomy may be combined with pelvic osteotomy.
Supportive Care:
-Supportive care involves educating parents on harness care, skin hygiene, and signs of complications (e.g., nerve palsy, skin breakdown)
-Regular clinical and radiological follow-up is essential to monitor progress and adjust treatment as needed
-Physiotherapy may be required post-treatment to regain full range of motion and strength.

Complications

Early Complications: Early complications of DDH management include: Pavlik harness-related issues: skin irritation, pressure sores, femoral nerve palsy (rare), avascular necrosis (rare, often due to overtreatment or improper positioning).
Late Complications:
-Late complications, especially if DDH is untreated or inadequately managed, can include: Osteoarthritis
-Avascular necrosis of the femoral head
-Irreparable joint damage
-Chronic hip pain
-Limp and gait abnormalities
-Hip dislocation recurrence.
Prevention Strategies:
-Prevention strategies focus on early detection through routine screening
-This includes: Clinical examination at birth and at subsequent well-child visits
-Universal ultrasound screening in high-risk populations or based on local protocols
-Promoting safe swaddling practices to avoid excessive hip adduction and extension
-Educating healthcare providers on the importance of early diagnosis.

Prognosis

Factors Affecting Prognosis:
-The prognosis of DDH is generally excellent when diagnosed and treated early
-Factors influencing outcome include: Age at diagnosis
-Severity of dysplasia
-Adequacy of reduction and stability
-Adherence to treatment
-Presence of associated anomalies.
Outcomes:
-With early and appropriate treatment, most infants achieve a stable hip with normal function and morphology
-Late diagnosis or treatment can lead to poorer outcomes, including early-onset osteoarthritis and the need for reconstructive surgery
-Approximately 80-90% of infants treated with the Pavlik harness before 3 months of age achieve a satisfactory reduction.
Follow Up:
-Long-term follow-up is crucial, especially for those with treated DDH or significant dysplasia
-This typically involves clinical assessments and serial radiographs until skeletal maturity to monitor for recurrence or the development of late complications like osteoarthritis
-Standard follow-up includes checks at 6 weeks, 3 months, 6 months, 1 year, and annually thereafter as clinically indicated.

Key Points

Exam Focus:
-Barlow's test assesses for provocation of dislocation
-Ortolani's test assesses for reduction of a dislocated hip
-Ultrasound is preferred for screening infants < 6 months
-Radiographs are used for infants > 6 months
-Pavlik harness is the primary treatment for infants < 6 months with unstable hips or significant dysplasia.
Clinical Pearls:
-Always perform hip examination in a relaxed infant, preferably on a warm surface
-Remember that a "clunk" on Ortolani's maneuver can be from a tight labrum or ligament, not necessarily a dislocated hip
-Monitor for signs of skin breakdown and neurovascular compromise with harness use.
Common Mistakes:
-Over-reliance on a single physical exam finding without imaging
-Delaying imaging in a persistently unstable or painful hip
-Improper application or prolonged immobilization with the Pavlik harness, leading to complications
-Failing to follow up adequately, missing early signs of treatment failure or recurrence.