Overview

Definition: Eczema herpeticum (EH) is a severe, disseminated herpes simplex virus (HSV) infection that occurs in individuals with compromised skin barrier function, most commonly atopic dermatitis.
Epidemiology:
-It can occur at any age but is more common in infants and young children
-Incidence is difficult to quantify precisely, but it is a recognized complication of severe atopic dermatitis
-Neonatal herpes is a distinct but related entity.
Clinical Significance:
-EH is a medical emergency due to its potential for rapid progression, systemic dissemination, and life-threatening complications including encephalitis, sepsis, and disseminated intravascular coagulation (DIC)
-Prompt diagnosis and treatment are crucial for favorable outcomes.

Clinical Presentation

Symptoms:
-Sudden onset of fever
-Malaise and lethargy
-Painful, itchy, vesicular rash that can rapidly evolve into pustules and erosions
-Worsening of underlying eczema
-Irritability in infants
-Signs of systemic illness.
Signs:
-Widespread, umbilicated vesicles and pustules, often superimposed on eczematous skin lesions
-Lesions are typically uniform in stage within a given area
-Regional lymphadenopathy
-Potential for mucocutaneous involvement (eyes, mouth, genitals)
-Signs of dehydration, sepsis, or organ involvement (e.g., neurological deficits).
Diagnostic Criteria:
-No universally agreed-upon formal criteria exist, but a diagnosis is strongly suspected in a patient with underlying eczema who develops a sudden onset of fever and widespread vesicular, pustular, and erosive lesions
-Viral confirmation is essential.

Diagnostic Approach

History Taking:
-Detailed history of underlying skin condition (onset, severity, treatments)
-Recent exposure to individuals with herpes simplex infection (herpes labialis, genital herpes)
-Fever, malaise, and progression of skin lesions
-Any eye involvement (redness, photophobia) is a critical red flag.
Physical Examination:
-Thorough skin examination to assess the distribution, morphology (vesicular, pustular, erosive), and stage of lesions
-Assess for signs of systemic illness: vital signs, hydration status, neurological examination, ocular examination.
Investigations:
-Viral isolation via viral culture (Tzanck smear with Giemsa stain may show multinucleated giant cells and intranuclear inclusions, but is less sensitive than PCR)
-Polymerase chain reaction (PCR) on vesicle fluid or biopsy is the gold standard for detecting HSV DNA and identifying HSV type (HSV-1 or HSV-2)
-Serology is generally not useful for acute diagnosis but may help in identifying primary HSV infection in some cases
-Blood tests may include complete blood count (CBC) with differential, electrolytes, and liver function tests to assess for systemic involvement.
Differential Diagnosis:
-Impetigo (bacterial infection, typically crusted lesions)
-Varicella (chickenpox, lesions are in different stages and typically distributed on trunk)
-Vaccinia (generalized vaccinia if recently vaccinated)
-Other forms of viral exanthems
-Candidiasis (intertriginous areas, satellite lesions).

Management

Initial Management:
-Hospitalization is often required, especially in severe cases, infants, or immunocompromised individuals
-Prompt initiation of intravenous antiviral therapy
-Fluid and electrolyte management
-Pain control.
Medical Management:
-Antiviral therapy is the cornerstone
-Intravenous acyclovir is the preferred agent
-Dosage for neonates: 20 mg/kg per dose given every 8 hours
-Dosage for older children: 10-15 mg/kg per dose given every 8 hours
-Duration of treatment is typically 7-14 days, or at least 7 days after lesions have crusted over and patient is afebrile
-Oral antiviral agents (valacyclovir, famciclovir) may be used for milder cases or as step-down therapy in select patients, guided by clinical response and local resistance patterns.
Supportive Care:
-Aggressive skin care to prevent secondary bacterial superinfection (e.g., dilute bleach baths may be considered in some cases of underlying eczema but should be used cautiously and under medical supervision)
-Wound care for erosions
-Nutritional support
-Close monitoring for signs of complications
-Isolation precautions if in a hospital setting to prevent transmission.
Management Of Underlying Eczema:
-Management of the underlying atopic dermatitis is critical for long-term prevention
-This includes regular emollients, topical corticosteroids as needed, and avoidance of triggers.

Complications

Early Complications:
-Secondary bacterial superinfection of skin lesions (e.g., Staphylococcus aureus, Streptococcus pyogenes)
-Dehydration
-Electrolyte imbalances
-Sepsis
-Disseminated intravascular coagulation (DIC)
-Pneumonitis.
Late Complications:
-Herpetic encephalitis (can lead to permanent neurological sequelae)
-Ocular involvement leading to corneal scarring and vision loss
-Scarring of the skin
-Recurrent episodes of EH.
Prevention Strategies:
-Aggressive management of underlying atopic dermatitis
-Patient and parental education on recognizing early signs of EH
-Prophylactic antiviral therapy may be considered in select high-risk individuals with severe, recurrent eczema, but this is not standard practice and requires careful risk-benefit assessment.

Prognosis

Factors Affecting Prognosis:
-Promptness of diagnosis and initiation of antiviral therapy
-Severity of systemic involvement
-Age of the patient (infants and neonates have higher mortality)
-Underlying immune status.
Outcomes:
-With prompt and appropriate treatment, most children recover fully
-However, severe cases can be associated with significant morbidity and mortality
-Neurological and ocular complications can lead to long-term disability.
Follow Up:
-Close follow-up is necessary to ensure complete resolution of lesions and to monitor for any long-term sequelae
-Management of the underlying eczema should be optimized
-Education on recognizing and managing future recurrences is vital.

Key Points

Exam Focus:
-EH is a viral dissemination in compromised skin, usually atopic dermatitis
-IV acyclovir is first-line
-Think sepsis, encephalitis, DIC as major complications
-Differentiate from impetigo and varicella.
Clinical Pearls:
-Always consider EH in a child with eczema presenting with fever and widespread vesicles, especially if lesions are uniform in stage
-Ocular involvement is a critical ophthalmological emergency
-Prompt IV acyclovir is paramount.
Common Mistakes:
-Delaying antiviral therapy due to diagnostic uncertainty
-Underestimating the severity and potential for systemic complications
-Inadequate management of the underlying eczema, leading to recurrence.