Overview

Definition:
-Functional constipation is defined by the Rome IV criteria as the presence of 2 or more of the following symptoms for at least 1 day per week in the preceding 3 months: infrequent stools, hard or lumpy stools, straining during defecation, sensation of incomplete evacuation, sensation of blockage or obstruction, and use of manual maneuvers to facilitate defecation
-Long-term maintenance dosing refers to the ongoing use of laxatives to prevent recurrence and maintain regular bowel movements after initial treatment of an acute episode.
Epidemiology:
-Functional constipation is a common problem in childhood, affecting an estimated 0.7% to 29.6% of children globally
-It is most prevalent in toddlers and preschool-aged children
-Recurrence rates are significant, highlighting the need for effective long-term management strategies.
Clinical Significance:
-Untreated or inadequately managed functional constipation can lead to significant morbidity in children, including pain, abdominal distension, fecal impaction, urinary tract infections, enuresis, and behavioral issues
-Chronic constipation can impact quality of life for both the child and their family, and proper long-term maintenance is crucial for preventing these complications and promoting healthy bowel habits.

Clinical Presentation

Symptoms:
-Infrequent stools (<3 per week)
-Hard, large, or difficult-to-pass stools
-Straining or pain during defecation
-Fecal soiling (encopresis) due to overflow incontinence
-Abdominal pain or cramping
-Reduced appetite
-Nausea
-Palpable fecal mass in the abdomen
-History of withholding stool.
Signs:
-Abdominal distension
-Palpable, firm stool in the lower abdomen or rectum on digital rectal examination
-Fecal soiling on underwear
-Perianal excoriation from soiling or wiping
-Rectal prolapse (less common)..
Diagnostic Criteria:
-Diagnosis is typically based on the Rome IV criteria for functional constipation in children
-Specific criteria include: 2 or more of the following symptoms for at least 1 day per week in the preceding 3 months: infrequent stools, hard or lumpy stools, straining, sensation of incomplete evacuation, sensation of blockage, manual maneuvers used to facilitate defecation
-Loose stools are not present
-Sufficient criteria for irritable bowel syndrome are not met
-Absence of organic disease upon medical history and physical examination
-For children younger than 4 years, symptoms must have begun at least 6 months prior to diagnosis and have occurred at least 1 time per week
-For toilet-trained children aged 4 years and older, symptoms must have occurred at least 1 time per week
-Red flags that suggest organic pathology include: onset of constipation in the first month of life, failure to thrive, bilious vomiting, abdominal distension, rectal bleeding beyond mild anal fissure bleeding, family history of Hirschsprung disease or celiac disease, abnormal neurological signs, or abnormal abdominal examination (e.g., a large mass)..

Diagnostic Approach

History Taking:
-Detailed history of bowel habits, including frequency, consistency, and ease of passage of stools
-Timing of onset of constipation
-Toilet training history
-Dietary intake (fiber and fluid intake)
-Medications (e.g., calcium supplements, anticholinergics)
-Presence of abdominal pain, nausea, vomiting, or poor appetite
-History of fecal soiling or encopresis
-Presence of red flags suggestive of organic causes: onset in infancy, failure to thrive, bilious vomiting, neurological deficits, sacral dimple, or abnormal anal tone
-Family history of gastrointestinal or endocrine disorders.
Physical Examination:
-General appearance: assess for failure to thrive or signs of systemic illness
-Abdominal examination: assess for distension, tenderness, and palpable fecal mass
-Rectal examination: assess for anal tone, presence of stool in the rectal vault, anal fissures, or prolapse
-In girls, assess for labial adhesions
-Neurological examination: particularly if red flags are present, to assess for spinal cord abnormalities or neuromuscular disorders..
Investigations:
-In most cases of functional constipation, investigations are not required if red flags are absent and the diagnosis is clear based on history and physical examination
-If red flags are present or if the diagnosis is uncertain, investigations may include: Complete blood count (CBC) to rule out anemia
-Electrolytes, calcium, phosphate, and alkaline phosphatase to assess for metabolic causes
-Thyroid function tests (TSH) to rule out hypothyroidism
-Celiac serology (anti-TTG antibodies)
-Abdominal X-ray to assess for fecal loading and impaction (not routine)
-Rectal manometry or anorectal manometry if Hirschsprung disease or functional defecation disorder is suspected
-Contrast enema or rectal biopsy if Hirschsprung disease is strongly suspected
-Biofeedback therapy may be indicated for children with functional defecation disorder
-For maintenance, routine investigations are not typically needed unless symptoms change or red flags emerge.
Differential Diagnosis:
-Hirschsprung disease
-Anal stenosis or stricture
-Hypothyroidism
-Hypercalcemia
-Celiac disease
-Neurological disorders (e.g., cerebral palsy, spinal cord lesions)
-Irritable bowel syndrome
-Inflammatory bowel disease (less common cause of constipation)
-Lead poisoning
-Meconium ileus (in neonates)..

Management

Initial Management:
-The initial management involves disimpaction, followed by a regular maintenance regimen
-Disimpaction may be achieved with oral osmotic laxatives (e.g., polyethylene glycol 3350) in higher doses, or through rectal administration of enemas or suppositories if oral therapy is insufficient
-Education of parents and child regarding constipation, toilet training, and the importance of consistent bowel movements is crucial.
Medical Management:
-Long-term maintenance therapy aims to prevent recurrence and maintain soft, easily passable stools
-The cornerstone of maintenance therapy is the use of osmotic laxatives
-Polyethylene Glycol 3350 (PEG 3350): This is the first-line agent
-Dosing: Typically starts at 0.5-1.5 g/kg/day, not to exceed 17 g/day for children under 2 years, and up to 34 g/day for children over 2 years
-The dose is adjusted to achieve soft stools daily or every other day
-Once regular bowel movements are established, the dose can be gradually reduced to the lowest effective dose for long-term maintenance
-Some children may require continuous daily use for months or even years
-Lactulose: A disaccharide laxative
-Dosing: Typically 1-2 mL/kg/day, divided into 1-2 doses, with a maximum of 20 mL/day
-Similar to PEG 3350, the dose is adjusted to maintain soft stools and then gradually reduced to the lowest effective maintenance dose
-It can cause bloating and flatulence
-Other agents: Stimulant laxatives (e.g., senna, bisacodyl) are generally reserved for short-term use or severe cases due to potential for dependence and cramping, but can be used cautiously as adjuncts in some maintenance plans under medical supervision
-Stool softeners like docusate sodium are less effective for functional constipation maintenance
-Mineral oil is generally not recommended due to risks of aspiration and vitamin malabsorption.
Surgical Management:
-Surgery is rarely indicated for functional constipation and is typically reserved for cases with underlying structural abnormalities that contribute to chronic constipation, such as severe anal stenosis or Hirschsprung disease that has not responded to medical management
-For functional constipation alone, surgical intervention is not an option.
Supportive Care:
-Dietary modifications: Increased intake of fiber-rich foods (fruits, vegetables, whole grains) and adequate fluid intake are essential adjuncts to laxative therapy
-Behavioral therapy: A regular toileting routine (e.g., sitting on the toilet for 5-10 minutes after meals) can help establish regular bowel habits
-Positive reinforcement for successful bowel movements is important
-Education: Comprehensive education for parents and children about the chronic nature of functional constipation, the rationale for long-term laxative use, and the importance of adherence is paramount
-Regular follow-up with a healthcare provider is necessary to monitor progress, adjust medication as needed, and address any concerns
-Regular physical activity also plays a role in promoting bowel motility.

Complications

Early Complications:
-Fecal impaction
-Rectal prolapse
-Abdominal pain and distension
-Fecal soiling (encopresis)
-Anal fissures
-Urinary tract infections (UTIs) due to pressure from impacted stool.
Late Complications:
-Chronic pain
-Behavioral issues related to soiling and embarrassment
-Poor quality of life
-Development of psychological distress or anxiety related to bowel function
-Potential for decreased bone mineral density if calcium intake is consistently poor due to avoidance of dairy
-Long-term reliance on laxatives, though generally safe with osmotic agents.
Prevention Strategies:
-Adherence to maintenance laxative therapy at the lowest effective dose
-Regular toileting routines
-Adequate fiber and fluid intake
-Behavioral interventions
-Regular medical follow-up to monitor for recurrence and adjust management
-Prompt treatment of any fecal impaction or soiling episodes.

Prognosis

Factors Affecting Prognosis:
-Adherence to treatment regimen
-Family support and education
-Presence of behavioral issues or psychological distress
-Extent and duration of chronic constipation prior to treatment
-Presence of underlying organic causes (though this is functional constipation)..
Outcomes:
-With consistent and appropriate long-term maintenance therapy and behavioral support, the prognosis for functional constipation is generally good
-Most children achieve regular bowel movements and resolution of symptoms
-However, it can be a chronic condition requiring management for several years, with a significant risk of relapse if treatment is discontinued prematurely or if lifestyle factors are not addressed
-Long-term maintenance doses can often be gradually reduced over time as children mature and develop more consistent bowel habits.
Follow Up:
-Follow-up appointments are crucial, initially every 1-3 months during active treatment and then every 6-12 months once stable
-The goal is to ensure continued compliance, monitor for recurrence of constipation or encopresis, assess for potential side effects of laxatives, and reinforce lifestyle and behavioral strategies
-Gradual tapering of laxative doses should be attempted periodically under medical supervision
-The duration of maintenance therapy varies significantly
-some children may require it for months, while others may need it for several years
-The decision to discontinue laxatives should be made by a healthcare provider in conjunction with the family, based on sustained symptom-free intervals and established healthy bowel habits.

Key Points

Exam Focus:
-Rome IV criteria for functional constipation in children
-First-line maintenance laxative: Polyethylene Glycol 3350 (PEG 3350)
-Standard maintenance dosing range for PEG 3350 (0.5-1.5 g/kg/day, max 17-34 g/day)
-Goal of maintenance therapy: soft, easily passable stools
-Importance of disimpaction before maintenance
-Role of fiber, fluids, and behavioral modification
-Red flags suggesting organic causes
-Management of encopresis
-Long-term management duration can be variable.
Clinical Pearls:
-Always rule out red flags before diagnosing functional constipation
-Education is key for adherence: explain to parents that laxatives are not habit-forming in this context and are necessary to break the pain-retention cycle
-Start low and go slow when adjusting PEG 3350 dose, aiming for soft stools every 1-2 days
-Consider gradual tapering of laxatives only when a child has been symptom-free for several months
-Be patient
-functional constipation is a chronic condition requiring long-term management
-Encopresis management requires a multifaceted approach including laxatives, timed toileting, and behavioral strategies.
Common Mistakes:
-Discontinuing laxatives too early, leading to relapse
-Underestimating the importance of disimpaction
-Insufficient education of parents and child regarding the condition and treatment plan
-Relying solely on diet and fluids without pharmacological support for maintenance
-Focusing only on stool frequency and not stool consistency and ease of passage
-Failing to identify and manage underlying behavioral or psychological factors
-Over-reliance on stimulant laxatives for long-term maintenance.