Overview

Definition:
-Hand-foot-and-mouth disease (HFMD) is a common, contagious viral illness typically affecting infants and young children
-It is characterized by fever, malaise, and a characteristic rash primarily on the hands, feet, and in the mouth.
Epidemiology:
-HFMD is most common in summer and autumn, though outbreaks can occur year-round
-It is caused by several strains of enteroviruses, most notably coxsackievirus A16 and enterovirus 71 (EV71)
-Transmission occurs through direct contact with respiratory secretions, blister fluid, or fecal-oral routes.
Clinical Significance:
-While typically a mild illness, HFMD is important for DNB and NEET SS candidates to understand due to its high prevalence in pediatric populations, potential for outbreaks, and rare but serious neurological complications, particularly with EV71 infection
-Effective symptomatic management, especially hydration and pain relief, is crucial for patient comfort and preventing dehydration.

Clinical Presentation

Symptoms:
-Fever typically appears first, followed by sore throat and loss of appetite
-Within 1-2 days, painful sores appear in the front of the mouth
-A non-itchy rash with small red spots, some blistering, develops on the palms of the hands and soles of the feet
-It may also appear on the knees, elbows, buttocks, or genital area
-Children may be irritable due to pain and discomfort.
Signs:
-Macular or papular rash on palms and soles
-vesicular or ulcerative lesions on oral mucosa (tongue, gums, buccal mucosa)
-mild cervical lymphadenopathy
-low-grade fever
-Vital signs are usually normal unless complications arise.
Diagnostic Criteria:
-Diagnosis is primarily clinical, based on the characteristic rash distribution and oral lesions in a febrile child
-No specific laboratory tests are routinely required for diagnosis, though viral PCR from throat or stool specimens can confirm the causative enterovirus in severe cases or outbreaks.

Diagnostic Approach

History Taking:
-Enquire about onset of fever, sore throat, rash development and distribution, appetite, oral intake, and any recent exposure to sick contacts
-Assess for signs of dehydration
-Red flags include neurological symptoms (seizures, lethargy, ataxia), respiratory distress, or severe vomiting.
Physical Examination:
-Examine for fever
-assess oral mucosa for characteristic vesicles and ulcers
-inspect hands and feet for maculopapular or vesicular rash
-check for lesions on buttocks, knees, and elbows
-palpate for lymphadenopathy
-evaluate hydration status (mucous membranes, skin turgor, urine output).
Investigations:
-Investigations are generally not required for uncomplicated HFMD
-In severe cases or during outbreaks, viral isolation and typing may be performed by PCR on throat swabs, stool, or cerebrospinal fluid (if meningitis is suspected)
-Complete blood count may show mild leukocytosis
-Electrolytes and renal function tests may be helpful if dehydration is suspected.
Differential Diagnosis:
-Other conditions with vesicular or ulcerative oral lesions and rash include herpangina (lesions predominantly on posterior pharynx), varicella (generalized rash, vesicles on trunk and limbs), herpes simplex stomatitis (more severe oral lesions, systemic symptoms), allergic reactions, and impetigo
-The characteristic distribution of rash on hands and feet is key to diagnosing HFMD.

Management

Initial Management:
-The primary goal is symptomatic relief and preventing complications
-This involves encouraging fluid intake to prevent dehydration and managing fever and pain.
Hydration:
-Adequate fluid intake is paramount
-Offer frequent small sips of cool liquids such as water, diluted fruit juices (avoid acidic ones like orange juice that can irritate mouth sores), or oral rehydration solutions (ORS)
-For infants, continue breastfeeding or formula feeding as tolerated
-Monitor urine output closely
-decreased output is an early sign of dehydration
-Severe dehydration may require intravenous fluid resuscitation.
Pain And Fever Control:
-Analgesics like paracetamol (acetaminophen) or ibuprofen can be used to manage fever and pain
-Dosing should be age and weight-appropriate according to standard pediatric guidelines
-Topical oral anesthetic gels or sprays may provide temporary relief for mouth sores, but caution is advised to avoid gagging or aspiration in younger children
-Offer soft, bland foods and cold liquids to ease swallowing.
Supportive Care:
-Maintain comfort through rest and a calm environment
-Good hand hygiene by caregivers is essential to prevent spread
-Monitor for signs of complications such as dehydration, neurological involvement (encephalitis, meningitis), or myocarditis
-Isolation of affected children during the highly contagious phase (when blisters are present) is recommended.

Complications

Early Complications:
-The most common complication is dehydration due to painful oral ulcers leading to reduced fluid intake
-Neurological complications are rare but serious, including aseptic meningitis, encephalitis, acute flaccid paralysis (especially with EV71), and Guillain-Barré syndrome.
Late Complications:
-Rarely, post-infectious sequelae or persistent neurological deficits can occur following severe EV71 infection
-Nail changes (onychodystrophy) or nail loss can occur a few weeks after the rash resolves but are generally transient.
Prevention Strategies:
-Good hygiene practices, including frequent handwashing with soap and water, especially after changing diapers and using the toilet, are critical
-Avoid close contact with infected individuals
-Prompt identification and isolation of symptomatic individuals can limit outbreaks in schools and childcare settings.

Prognosis

Factors Affecting Prognosis:
-Prognosis is generally excellent for most cases caused by coxsackievirus A16, with full recovery within 7-10 days
-Cases caused by enterovirus 71 have a higher risk of severe neurological and systemic complications, which can lead to significant morbidity or mortality.
Outcomes:
-Most children recover fully with supportive care
-Severe complications are uncommon
-Long-term sequelae are rare, primarily associated with EV71 infection.
Follow Up:
-Routine follow-up is not typically required for uncomplicated HFMD
-However, children with severe complications or suspected neurological involvement need close medical supervision and follow-up by specialists.

Key Points

Exam Focus:
-DNB/NEET SS candidates should focus on the clinical presentation, distinguishing features from herpangina and other vesicular rashes, and the management of hydration and pain
-Recognize EV71 as a potential cause of severe neurological complications.
Clinical Pearls:
-Emphasize maintaining hydration by offering fluids frequently and in small amounts
-Avoid acidic or salty foods that can exacerbate oral pain
-Monitor urine output as a key indicator of hydration status
-Educate parents on hygiene practices to prevent spread.
Common Mistakes:
-Overlooking early signs of dehydration in infants and young children
-Inadequate pain management leading to poor oral intake
-Misdiagnosing HFMD due to atypical rash presentations or confusion with other viral exanthems
-Failure to consider EV71 in cases with neurological signs.