Overview

Definition:
-Necrotizing Enterocolitis (NEC) is a devastating gastrointestinal emergency primarily affecting premature infants, characterized by intestinal inflammation, ischemia, and necrosis
-Surgical intervention is often required for advanced NEC.
Epidemiology:
-NEC is the most common non-congenital surgical emergency in neonates, with an incidence of 1-4 per 1000 live births, significantly higher in very low birth weight infants (<1000g)
-Mortality rates can exceed 30% in surgically treated cases.
Clinical Significance:
-Early recognition of NEC and timely surgical decision-making are critical for improving survival and reducing long-term morbidity
-Effective ostomy care is paramount for patient recovery and preventing complications post-surgery.

Surgical Indications

Indications Medical Refractory:
-Failure to improve despite maximal medical management (bowel rest, antibiotics, nasogastric decompression, fluid resuscitation) for 24-48 hours
-Persistent abdominal distension, bloody stools, and hemodynamic instability.
Indications Perforation: Radiographic evidence of pneumoperitoneum (free air in the abdominal cavity) on plain abdominal X-ray is an absolute indication for immediate surgery.
Indications Abdominal Wall Signs: Abdominal wall erythema, edema, induration, or a rigid abdomen suggest transmural bowel necrosis and perforation, necessitating surgical exploration.
Indications Other Deterioration: Progressive metabolic acidosis unresponsive to treatment, worsening thrombocytopenia, coagulopathy, or signs of sepsis and shock despite intensive medical therapy.

Diagnostic Approach

History Taking:
-Detailed feeding history (prematurity, formula vs
-breast milk, timing of feeds)
-Onset and progression of symptoms
-Previous episodes of NEC
-Maternal and birth history.
Physical Examination:
-Abdominal assessment: distension, tenderness, guarding, rigidity, decreased bowel sounds or absent sounds
-Presence of abdominal wall discoloration (erythema, purpura, cyanosis)
-Rectal examination for blood
-Vital signs: tachycardia, hypotension, hypothermia/fever, respiratory distress.
Investigations:
-Abdominal X-ray: initial imaging of choice, looking for bowel distension, thickened bowel wall, pneumatosis intestinalis, portal venous gas, and free air
-Ultrasound: can be useful for detecting free fluid and ascites
-Blood tests: Complete Blood Count (CBC) for leukocytosis/leukopenia, thrombocytopenia
-electrolytes, arterial blood gases (ABGs) for acidosis
-C-reactive protein (CRP) for inflammation
-coagulation profile.
Differential Diagnosis: Other causes of abdominal distension and feeding intolerance in neonates, including prematurity-related issues (immature gut motility), sepsis, congenital intestinal anomalies (e.g., malrotation with volvulus, Hirschsprung disease), intussusception, or surgical abdomen from other causes.

Surgical Management

Initial Surgical Steps:
-Laparotomy or limited enterotomy with initial decompression of distended bowel segments
-Lavage of the peritoneal cavity if contaminated
-Identification of necrotic or perforated bowel segments.
Resection And Anastomosis:
-Resection of all frankly necrotic or perforated bowel
-Decision regarding primary anastomosis versus diversion with ostomy is based on the extent of involvement, infant's stability, and surgeon's judgment
-Limited resection is preferred to preserve as much bowel as possible.
Diversion Ostomy:
-Creation of a stoma (ileostomy or colostomy) is common, especially in critically ill infants or when the distal bowel is compromised
-This diverts fecal stream and allows the defunctionalized bowel to heal.
Secondary Anastomosis: If an ostomy is created, a plan for eventual stoma reversal and intestinal anastomosis is made, typically after the infant has recovered and gained weight.

Ostomy Care

Stoma Assessment:
-Regular visual inspection of the stoma: color (should be pink to red), moisture, and any signs of retraction, prolapse, stenosis, or ischemia
-Assess surrounding skin for irritation, erythema, or breakdown.
Ostomy Appliance Selection:
-Appropriate ostomy pouching system is crucial
-Options include one-piece or two-piece systems
-Skin barrier (wafer) should be cut to fit snugly around the stoma without constricting it
-Convexity may be needed for retracted stomas.
Skin Care:
-Clean the peristomal skin gently with warm water or a mild, non-alcoholic cleanser
-Dry the skin thoroughly
-Apply a skin barrier paste or ring as needed to fill uneven skin contours
-Protect the skin from stoma output with barrier creams or sprays.
Output Management:
-Monitor stoma output: consistency, volume, and any signs of malabsorption
-Fluid and electrolyte balance must be carefully managed, especially with high-output ileostomies
-Nutritional support, including parenteral or enteral feeding, is essential
-Education of parents/caregivers on stoma care is vital for home management.

Complications

Surgical Complications: Intra-abdominal abscess, wound infection, anastomotic leak, adhesions, bowel obstruction, stomal complications (retraction, prolapse, stenosis, fistula), short bowel syndrome.
Long Term Sequelae: Growth failure, malabsorption, neurodevelopmental delays, increased risk of gastrointestinal infections, increased incidence of surgical re-operations, electrolyte imbalances.
Prevention And Monitoring:
-Strict aseptic technique during surgery and stoma management
-Early recognition and management of stomal issues
-Aggressive nutritional support
-Close monitoring of fluid and electrolyte status
-Serial abdominal examinations to detect early signs of recurrence or complications.

Key Points

Exam Focus:
-Absolute surgical indication: pneumoperitoneum
-Key decision: resection vs
-diversion
-Ostomy characteristics (color, moisture)
-Peristomal skin integrity is crucial.
Clinical Pearls:
-When in doubt, explore! Preserve bowel length whenever possible
-Timely ostomy creation can be life-saving
-Parental education is a core component of ostomy care.
Common Mistakes:
-Delaying surgery in medically refractory NEC
-Inadequate bowel resection
-Poorly fitted ostomy appliances leading to skin breakdown
-Underestimating fluid and electrolyte losses from stomas.