Overview

Definition:
-Seizure first aid for families involving rescue medications refers to the immediate administration of specific anti-seizure drugs by caregivers at home to terminate prolonged or recurrent seizures in a child, typically administered via non-intravenous routes
-This is crucial for managing convulsive status epilepticus in a timely manner
-Febrile seizures are common in children and may require rescue medication if prolonged or recurrent
-For children with epilepsy, breakthrough seizures may also necessitate rescue therapy.
Epidemiology:
-Convulsive status epilepticus occurs in approximately 4-10 per 100,000 children annually
-Febrile seizures affect 2-5% of children, with prolonged or recurrent seizures occurring in a subset
-Families of children with epilepsy and those prone to febrile seizures are candidates for home-based rescue medication protocols
-The majority of prolonged seizures in children are convulsive.
Clinical Significance:
-Promptly stopping a prolonged seizure is critical to prevent neurological injury, secondary complications like hyperthermia or hypoxia, and the development of status epilepticus
-Educating families on the appropriate use of rescue medications empowers them to act effectively in emergency situations, potentially reducing emergency room visits and hospital admissions
-It is a vital component of comprehensive epilepsy and febrile seizure management for pediatric residents preparing for board examinations.

Rescue Medications

Options:
-Commonly prescribed rescue medications include benzodiazepines due to their rapid onset of action
-These include rectal diazepam, buccal midazolam, and intranasal midazolam
-Oral formulations like lorazepam are also used, but absorption can be slower and more variable
-The choice of medication and route depends on availability, ease of administration, local protocols, and physician preference.
Mechanism Of Action:
-Benzodiazepines enhance the inhibitory effects of gamma-aminobutyric acid (GABA) at the GABA-A receptor, leading to hyperpolarization of neurons and reduced neuronal excitability, thus terminating the seizure
-They work by increasing the frequency of chloride channel opening.
Indication For Use:
-Rescue medications are indicated for prolonged seizures, typically defined as seizures lasting longer than 5 minutes, or for recurrent seizures occurring within a short period (e.g., multiple seizures within an hour) without the child regaining consciousness between episodes
-Specific protocols will outline precise timeframes and seizure patterns
-Parents should always call emergency medical services after administering rescue medication, especially if the seizure does not stop promptly.

Administration And Dosing Pediatrics

Rectal Diazepam:
-Dosage is typically 0.3-0.5 mg/kg per dose, with a maximum single dose of 10 mg
-It can be administered every 5-10 minutes for up to 3 doses if needed, or as per specific physician order
-Administration involves inserting the pre-filled syringe into the rectum
-Note that absorption can be variable.
Buccal Midazolam:
-Dosage is typically 0.1-0.3 mg/kg per dose, with a maximum of 10 mg per dose
-It can be given every 5-10 minutes for up to 3 doses
-The liquid formulation is administered to the buccal (inside of the cheek) mucosa
-It offers faster absorption than oral and is often preferred over rectal routes due to ease of administration and better tolerability.
Intranasal Midazolam:
-Dosage is typically 0.2 mg/kg per dose, with a maximum of 10 mg per dose
-It can be administered every 5-10 minutes for up to 3 doses
-The medication is sprayed into one or both nostrils
-This route also provides rapid absorption and is well-tolerated
-It is a valuable alternative when buccal administration is difficult.
Oral Lorazepam:
-Dosage is typically 0.1 mg/kg per dose, with a maximum of 4 mg per dose
-It can be administered every 5-10 minutes for up to 3 doses
-While effective, oral absorption can be unpredictable and slower than other routes, making it less ideal for acute rescue scenarios where rapid termination is paramount.

Family Education And Training

Importance Of Training:
-Comprehensive training for families is essential, including understanding when and how to administer the medication, potential side effects, and when to seek emergency medical help
-Training should be hands-on where possible, with demonstration and return demonstration of administration techniques
-This preparedness is key for residents to advise families effectively.
Key Teaching Points:
-Educate families on recognizing seizure types that require intervention, understanding the prescribed medication and its correct dosage, proper administration technique for the chosen route, signs of effective termination of seizure, and potential side effects (e.g., drowsiness, lethargy)
-Emphasize calling emergency services (108/102 in India) after administration, regardless of seizure cessation.
Storage And Dispensing:
-Families must be instructed on proper storage of rescue medications (e.g., at room temperature, away from light, out of reach of children)
-Prescription details should be clearly documented
-The importance of having medication readily accessible during potential seizure events, such as during travel or at school, should be stressed
-Regular checks for expiry dates are vital.
Emergency Protocols:
-Families should have a written emergency plan from their physician, outlining the specific medication, dosage, frequency of administration, and when to call emergency medical services or attend the nearest hospital
-They should be educated on how to provide clear information to emergency responders about the seizure event and the medication administered.

Complications And Side Effects

Common Side Effects:
-The most common side effects are central nervous system depression, including somnolence, lethargy, ataxia, and confusion
-Respiratory depression can occur, particularly with higher doses or co-administration of other sedating medications
-Hypotension is also a possible adverse effect.
Rare But Serious Complications:
-Rare complications include paradoxical excitement, laryngospasm, and the development of respiratory arrest
-Long-term use or frequent administration might be associated with tolerance and dependence, though this is less common with intermittent rescue therapy
-The risk of aspiration exists if the child is unable to protect their airway.
Management Of Adverse Effects:
-Mild somnolence and lethargy are often expected and transient
-If significant respiratory depression or hypotension occurs, immediate medical attention is required
-Airway support and, if necessary, reversal agents (like flumazenil for benzodiazepine overdose, though rarely used in rescue scenarios due to risk of rebound seizures) may be considered by medical professionals
-Close monitoring after administration is crucial.

Role Of Healthcare Professionals

Physician Responsibility:
-Physicians are responsible for diagnosing the underlying cause of seizures, determining the need for rescue medication, prescribing the appropriate agent and dosage, and providing comprehensive education to families
-They must also ensure appropriate follow-up and re-evaluation of the treatment plan
-This includes providing clear, written instructions for home use.
Nurse Role In Education:
-Pediatric nurses play a crucial role in reinforcing physician instructions, demonstrating medication administration techniques, answering family questions, and assessing family understanding and preparedness
-They are frontline educators for families and essential in ensuring adherence to the treatment plan.
Pharmacist Contribution:
-Pharmacists ensure that the correct medication and dosage are dispensed and can provide additional counseling to families regarding storage, administration, and potential drug interactions
-They are a valuable resource for families regarding their prescribed medications
-Pharmacists also play a role in advising physicians on appropriate formulations and dosages.

Key Points

Exam Focus:
-Focus on the indications for rescue medication, preferred agents (benzodiazepines), common routes of administration (rectal, buccal, intranasal), typical pediatric dosages, and the importance of family education
-Understand the definition of status epilepticus and the immediate management goals
-Recall that these medications are for terminating prolonged seizures, not for chronic seizure prevention.
Clinical Pearls:
-Always emphasize calling emergency services after administering rescue medication
-Ensure families know the difference between a typical brief febrile seizure and one requiring intervention
-Practice return demonstration for administration techniques with families
-Keep rescue medications accessible and check expiry dates regularly
-Be aware of potential for sedation and respiratory depression and advise parents accordingly.
Common Mistakes:
-Mistakes include administering rescue medication for brief or typical seizures, incorrect dosage calculation, improper administration technique leading to ineffectiveness, delaying emergency medical services contact, and not checking medication expiry dates
-Failure to adequately educate families about side effects and when to seek further medical help is also a significant error.