Overview

Definition:
-Supraventricular tachycardia (SVT) in infants is a sustained heart rhythm with a ventricular rate typically exceeding 180-220 beats per minute, originating from above the ventricles
-Vagal maneuvers are non-pharmacological techniques that stimulate the vagus nerve to slow heart rate.
Epidemiology:
-SVT is the most common sustained tachyarrhythmia in infancy, with an incidence of 1 in 2500 live births
-It often presents within the first few months of life
-Recurrence is common, and prompt recognition and management are crucial.
Clinical Significance:
-Unrecognized or untreated SVT in infants can lead to hemodynamic instability, heart failure, profound irritability, feeding difficulties, and potentially cardiogenic shock
-Effective management, including appropriate vagal maneuvers, is vital for infant well-being and reduces the need for immediate pharmacological intervention.

Clinical Presentation

Symptoms:
-Sudden onset of rapid heart rate
-Infant appears pale and irritable
-Poor feeding
-Tachypnea or difficulty breathing
-Vomiting
-Lethargy or unresponsiveness
-In severe cases, signs of shock: cool extremities, decreased perfusion, hypotension.
Signs:
-Heart rate > 180-220 bpm, often regular and narrow complex on palpation of pulse or auscultation
-May have a short RP interval on ECG
-Possible signs of poor perfusion: delayed capillary refill, mottled skin
-Signs of heart failure: hepatomegaly, pulmonary rales.
Diagnostic Criteria:
-Diagnosis is confirmed by electrocardiogram (ECG) demonstrating a narrow-complex tachycardia with a heart rate above established infant norms, usually with absent or inverted P waves in inferior leads
-Differentiating between sinus tachycardia and SVT is critical.

Diagnostic Approach

History Taking:
-Focus on the onset and duration of symptoms
-Any prior episodes
-Maternal history of arrhythmias
-Family history of sudden cardiac death or arrhythmias
-Recent febrile illness or dehydration.
Physical Examination:
-Assess infant's general appearance, perfusion, and respiratory status
-Palpate peripheral pulses for rate and regularity
-Auscultate heart sounds, noting rate, rhythm, and presence of murmurs
-Assess for hepatomegaly and lung auscultation findings.
Investigations:
-A 12-lead ECG is paramount to confirm the diagnosis, determine the rhythm (e.g., AVNRT, AVRT), and assess hemodynamic stability
-Echocardiography may be performed to evaluate for structural heart disease if the diagnosis is unclear or if there are signs of heart failure.
Differential Diagnosis:
-Sinus tachycardia (due to fever, crying, dehydration, anxiety)
-Other supraventricular arrhythmias like atrial flutter or fibrillation (rare in infants)
-Ventricular tachycardia (very rare in infants without structural heart disease)
-Sepsis.

Management

Initial Management:
-Assess hemodynamic stability
-If stable, attempt vagal maneuvers first
-If unstable, proceed to immediate synchronized cardioversion
-Ensure IV access and resuscitation equipment are readily available.
Vagal Maneuvers:
-Techniques include: ice pack to the face (occlusion of nares and mouth, but allow breathing)
-Stimulating the pharynx or posterior palate with a tongue depressor or cotton swab
-Valsalva maneuver (if age-appropriate and feasible, typically older infants)
-**Crucially, these must be performed carefully in infants to avoid hypoxia.**
Pharmacological Management:
-If vagal maneuvers fail or are not feasible: Adenosine is the first-line drug
-Administered as a rapid IV bolus (0.1 mg/kg, then 0.2 mg/kg if needed) followed by a saline flush
-Amiodarone or procainamide may be used if adenosine is ineffective or contraindicated.
Supportive Care:
-Continuous cardiac monitoring
-Oxygen supplementation if hypoxic
-Management of heart failure if present
-Close observation for recurrence or complications
-Hydration and nutritional support.

Complications

Early Complications:
-Refractory SVT despite interventions
-Hemodynamic collapse leading to shock
-Paradoxical bradycardia with AV nodal blocking agents
-Hypotension from cardioversion.
Late Complications:
-Recurrence of SVT episodes
-Development of heart failure
-Potential for increased risk of arrhythmias later in life, especially if underlying structural heart disease exists.
Prevention Strategies:
-For recurrent SVT, long-term antiarrhythmic therapy (e.g., flecainide, sotalol) may be initiated
-Catheter ablation is an option for refractory or frequent symptomatic episodes, especially in older infants and children
-Education of parents on recognizing symptoms and when to seek medical attention.

Prognosis

Factors Affecting Prognosis:
-Hemodynamic stability at presentation
-Presence of underlying structural heart disease
-Effectiveness of initial management
-Frequency and duration of SVT episodes.
Outcomes:
-Most infants with SVT respond well to initial management with vagal maneuvers or adenosine
-Those with structurally normal hearts have an excellent prognosis after successful treatment and often do not require long-term therapy or ablation.
Follow Up:
-Regular cardiology follow-up is recommended to monitor for recurrence, assess growth and development, and re-evaluate the need for ongoing treatment or ablation
-Parents should be educated on symptom recognition and emergency contact protocols.

Key Points

Exam Focus:
-Vagal maneuvers are the first-line treatment for stable infants with SVT
-Adenosine is the drug of choice if maneuvers fail
-Differentiate SVT from sinus tachycardia
-ECG findings are diagnostic
-Unstable infants require immediate cardioversion.
Clinical Pearls:
-Be quick and decisive with interventions
-Ice pack to the face is often effective but monitor for hypoxia
-Adenosine has a very short half-life, hence the rapid flush is crucial
-Always have resuscitation equipment ready.
Common Mistakes:
-Delaying intervention in unstable infants
-Incorrectly administering adenosine (too slow, wrong dose)
-Misinterpreting sinus tachycardia as SVT
-Forgetting to consider underlying causes like sepsis.