Overview

Definition:
-Post-exposure prophylaxis (PEP) for varicella-zoster virus (VZV) in siblings aims to prevent or attenuate infection after exposure to an index case of chickenpox
-This typically involves administering the varicella vaccine or, in select high-risk individuals, varicella-zoster immune globulin (VZIG).
Epidemiology:
-Varicella is highly contagious, with siblings of an infected child having a very high risk of transmission (up to 90%)
-In India, varicella is endemic, with significant outbreaks occurring
-The incidence is highest in children aged 5-10 years
-Vaccination has significantly reduced disease incidence in vaccinated populations.
Clinical Significance:
-Preventing varicella in susceptible siblings is crucial to avoid illness, potential complications (pneumonia, encephalitis, secondary bacterial infections), and to reduce further spread within households and communities
-It is particularly important for siblings who are immunocompromised or too young to be vaccinated
-This topic is frequently tested in DNB and NEET SS examinations, requiring a thorough understanding of current guidelines.

Risk Assessment And Indications

Identifying Exposure: A sibling is considered exposed if they have had close contact with a person with confirmed or probable varicella within the contagious period (typically 1-2 days before rash onset to the crusting of all lesions).
Susceptibility Assessment:
-Determine the sibling's immune status: documented history of varicella, documented vaccination with 2 doses of varicella vaccine, or serological evidence of immunity
-Susceptible individuals are those without any of these criteria.
Indications For Vaccine PEP:
-Varicella vaccine (live attenuated) is recommended for susceptible siblings within 72 hours (ideally 48 hours) of exposure if they are immunocompetent
-It can be given up to 5 days post-exposure with some potential benefit
-This aims to prevent infection or reduce severity.
Indications For VZIG:
-VZIG is reserved for high-risk, susceptible individuals who cannot receive the vaccine or in whom the vaccine may be less effective
-This includes immunocompromised children, neonates born to mothers with varicella around delivery, pregnant women exposed to varicella, and premature infants born at <28 weeks gestation or weighing <1000g
-VZIG must be administered within 96 hours of exposure.

Management Strategies

Vaccine Administration:
-For immunocompetent, susceptible siblings, administer one dose of varicella vaccine (live attenuated)
-The dose is typically 0.5 mL subcutaneously
-For PEP, it is usually one dose, even if the child has had one dose previously, as PEP doses may be spaced differently.
VZIG Administration:
-VZIG is given intramuscularly at a dose of 125 units/10 kg body weight, with a maximum dose of 625 units
-It provides passive immunity and is primarily used for prophylaxis in high-risk individuals.
Supportive Care:
-Regardless of PEP, symptomatic management is crucial
-This includes antipyretics (paracetamol/ibuprofen), pruritus relief (calamine lotion, oral antihistamines), and monitoring for signs of complications
-Avoid aspirin due to the risk of Reye's syndrome.
Isolation Precautions:
-The index case should be isolated until all lesions have crusted over
-Susceptible siblings should also avoid contact with immunocompromised individuals until they have either developed immunity or recovered from any potential infection.

Vaccine Vs VZIG Considerations

Vaccine Advantages:
-Induces active immunity, providing long-lasting protection
-Generally well-tolerated and readily available.
Vaccine Disadvantages:
-Live attenuated virus, contraindicated in severely immunocompromised individuals
-Onset of protection may be slower than VZIG.
VZIG Advantages:
-Provides immediate passive immunity, suitable for immunocompromised individuals
-Can be effective up to 96 hours post-exposure.
VZIG Disadvantages:
-Provides temporary immunity, can interfere with the response to live vaccines given concurrently or soon after
-More expensive and less readily available than the vaccine
-Potential for anaphylaxis (rare).

Prognosis And Follow Up

Outcomes With Vaccine PEP:
-If given within 72 hours, the vaccine can prevent varicella entirely in about 50-80% of cases or significantly attenuate the disease, leading to fewer lesions and milder symptoms
-A breakthrough case may still occur but is typically less severe.
Outcomes With VZIG:
-VZIG can prevent or attenuate varicella in high-risk individuals, reducing the risk of severe disease and complications
-It is a bridge to allow time for immune reconstitution or alternative treatments.
Monitoring For Breakthrough Infection:
-Susceptible siblings who receive PEP should be monitored for the development of varicella lesions
-Even with PEP, mild or atypical cases can occur.
Long Term Immunity:
-The varicella vaccine provides long-term immunity, similar to that after natural infection
-VZIG provides only temporary protection.

Key Points

Exam Focus:
-Key decision points revolve around the timing of exposure, the sibling's immune status, and the choice between vaccine and VZIG
-Understand contraindications for live vaccines
-Dosing of VZIG is critical.
Clinical Pearls:
-Always confirm vaccination status and previous varicella history
-Prompt administration of vaccine (within 72 hours) is paramount for immunocompetent siblings
-Consider immunocompromised status carefully for VZIG indication
-Educate parents on isolation and monitoring.
Common Mistakes:
-Delayed administration of PEP
-Administering live vaccine to severely immunocompromised patients without proper consultation
-Incorrect VZIG dosing or administration window
-Failing to consider breakthrough infections
-Not documenting previous varicella or vaccination.