Overview

Definition:
-Gallstone ileus is a rare mechanical bowel obstruction that occurs when a gallstone erodes through the gallbladder wall and into the small intestine, creating a cholecystoenteric fistula and subsequently obstructing the bowel lumen
-Enterolithotomy is the surgical procedure to remove the impacted gallstone from the intestine.
Epidemiology:
-It is an uncommon complication of cholelithiasis, accounting for 1-4% of all mechanical small bowel obstructions
-The incidence increases with age, with most patients being elderly females (peak incidence in the 7th to 8th decades)
-Pre-existing comorbidities are common.
Clinical Significance:
-Gallstone ileus is a surgical emergency associated with high morbidity and mortality (reported rates range from 12% to 30%)
-Early recognition and prompt surgical intervention are critical for improving patient outcomes and reducing complications.

Clinical Presentation

Symptoms:
-Abdominal pain, typically colicky and epigastric or periumbilical
-Nausea and vomiting, often bilious
-Abdominal distension
-Constipation or obstipation (absence of flatus and stool)
-Weight loss and malnutrition in chronic cases
-Fever may suggest associated inflammation or infection.
Signs:
-Distended abdomen with tympany
-Tenderness on palpation, which may be diffuse or localized
-Signs of dehydration and electrolyte imbalance
-Absent bowel sounds or hyperactive high-pitched bowel sounds may be present initially
-A palpable abdominal mass can sometimes be felt.
Diagnostic Criteria:
-Diagnosis is primarily based on clinical suspicion combined with imaging findings
-The Rigler's triad (pneumobilia, ectopic gallstone, and bowel obstruction) is pathognomonic but not always present
-Confirmation often requires demonstration of the fistula and the obstructing stone on imaging.

Diagnostic Approach

History Taking:
-Focus on symptoms of bowel obstruction, duration, and progression
-Inquire about prior episodes of biliary colic, jaundice, or gallbladder disease
-Assess for comorbidities such as diabetes, cardiovascular disease, and immunosuppression
-Note any recent weight loss or changes in bowel habits.
Physical Examination:
-Thorough abdominal examination for distension, tenderness, guarding, rigidity, and palpable masses
-Assess for signs of dehydration (dry mucous membranes, decreased skin turgor, postural hypotension)
-Perform a digital rectal examination to rule out distal obstruction or impaction.
Investigations:
-Plain abdominal radiography may show signs of bowel obstruction (dilated loops of bowel, air-fluid levels) and may reveal calcified gallstones or pneumobilia
-Computed tomography (CT) scan is the investigation of choice, demonstrating the gallstone, fistula, bowel obstruction, and extent of disease
-it also helps in identifying other causes of obstruction
-Ultrasound may show dilated bile ducts or gallstones but is less sensitive for gallstone ileus itself
-Laboratory tests include complete blood count, electrolytes, renal function tests, and liver function tests to assess for dehydration, infection, and biliary involvement.
Differential Diagnosis:
-Other causes of small bowel obstruction: adhesions, hernias, malignancy, intussusception, volvulus
-Bouveret's syndrome (gastric outlet obstruction by a gallstone)
-Inflammation of the bowel or appendix
-Appendicular or diverticular abscess.

Management

Initial Management:
-Immediate resuscitation with intravenous fluids to correct dehydration and electrolyte imbalances
-Nasogastric tube insertion for decompression of the stomach and small bowel
-Pain management with analgesics
-Broad-spectrum antibiotics should be initiated if signs of infection are present.
Medical Management:
-Primarily supportive care
-Medical management alone is rarely effective for definitive treatment of gallstone ileus
-It focuses on stabilizing the patient and managing complications.
Surgical Management:
-Surgical intervention is indicated for all patients with confirmed gallstone ileus
-The surgical approach aims to relieve the obstruction and, ideally, address the fistula
-The primary surgical procedure involves enterolithotomy to remove the obstructing stone
-Options for fistula management include: 1) Enterolithotomy alone (most common, especially in high-risk patients), allowing spontaneous closure of the fistula
-2) Enterolithotomy with cholecystectomy and fistula repair (more definitive but increases operative time and risk, reserved for stable patients)
-3) Laparoscopic approaches are being increasingly used but may be challenging due to inflammation and adhesions.
Supportive Care:
-Close monitoring of vital signs, fluid balance, and electrolyte levels
-Nutritional support, including parenteral nutrition if prolonged ileus or malabsorption is anticipated
-Postoperative physiotherapy to prevent pulmonary complications
-Pain control and wound care.

Complications

Early Complications:
-Bowel ischemia and perforation at the site of obstruction
-Sepsis
-Anastomotic leak if enterotomy or resection is performed
-Intra-abdominal abscess
-Prolonged ileus
-Dehiscence of enterotomy closure.
Late Complications:
-Recurrent gallstone ileus if the fistula is not closed
-Malabsorption and weight loss
-Incisional hernia
-Chronic abdominal pain
-Stricture formation at the site of enterotomy or fistula.
Prevention Strategies:
-Timely and appropriate management of symptomatic gallstones to prevent the formation of cholecystoenteric fistulas
-Prophylactic cholecystectomy in asymptomatic patients with certain risk factors, although this is a debated topic
-However, once gallstone ileus is diagnosed, the goal is to prevent complications through prompt and effective surgical management and meticulous postoperative care.

Prognosis

Factors Affecting Prognosis:
-Patient's age and comorbidities significantly impact prognosis
-Delay in diagnosis and treatment is associated with higher mortality
-The extent of bowel involvement and the development of complications like perforation or sepsis worsen the outcome
-The surgical approach chosen also plays a role.
Outcomes:
-With prompt diagnosis and surgical management, mortality rates can be reduced
-Patients who are surgically treated generally have a good outcome, especially if complications are avoided
-However, elderly and infirm patients have a poorer prognosis.
Follow Up:
-Postoperative follow-up typically involves monitoring for wound healing, return of bowel function, and signs of recurrent obstruction or malabsorption
-Long-term follow-up may be indicated for patients with persistent symptoms or if a conservative approach to fistula management was chosen, to ensure spontaneous closure or to address late complications.

Key Points

Exam Focus:
-Remember Rigler's triad: pneumobilia, ectopic gallstone, bowel obstruction
-Gallstone ileus is a complication of cholelithiasis leading to mechanical obstruction via a cholecystoenteric fistula
-Elderly females are most commonly affected
-CT scan is the gold standard for diagnosis.
Clinical Pearls:
-Suspect gallstone ileus in elderly patients with unexplained bowel obstruction and no history of prior abdominal surgery
-Consider pneumobilia on imaging even in the absence of a visible stone within the bowel lumen
-Enterolithotomy alone is often sufficient and safer in frail patients.
Common Mistakes:
-Delayed diagnosis due to attributing symptoms to other common gastrointestinal issues
-Inadequate resuscitation before surgery
-Overtreatment in high-risk patients by opting for a two-stage procedure when a single-stage enterolithotomy would suffice
-Failure to consider gallstone ileus in the differential diagnosis of bowel obstruction in the elderly.