Overview

Definition:
-May-Thurner stent thrombosis refers to the acute or subacute occlusion of a previously placed endovascular stent in the iliac vein, typically within the context of May-Thurner syndrome (also known as iliac vein compression syndrome)
-This syndrome involves compression of the left iliac vein by the overlying right iliac artery, predisposing to deep vein thrombosis (DVT)
-Stenting is often used to relieve this compression, and subsequent thrombosis of the stent is a serious complication requiring urgent intervention.
Epidemiology:
-May-Thurner syndrome is present in up to 30% of individuals, with a higher prevalence in women
-Stent thrombosis is a rare but significant complication of iliac vein stenting, with reported rates varying between 1-5% in the short-to-medium term, depending on stent type, antithrombotic regimen, and patient factors
-Risk factors for stent thrombosis include hypercoagulable states, inadequate anticoagulation, undertreatment of May-Thurner syndrome, suboptimal stent deployment, and intimal hyperplasia.
Clinical Significance:
-May-Thurner stent thrombosis represents a limb-threatening emergency
-It can lead to severe acute venous insufficiency, post-thrombotic syndrome, pulmonary embolism (PE), and in rare cases, venous gangrene
-Prompt recognition and effective surgical rescue are critical to restore venous outflow, prevent further complications, and salvage limb viability
-This condition is a high-yield topic for DNB and NEET SS examinations due to its complexity and critical management.

Clinical Presentation

Symptoms:
-Sudden onset of severe ipsilateral leg swelling
-Increasing leg pain and heaviness
-Skin discoloration (erythema, cyanosis)
-Reduced distal pulses
-Fever
-Dyspnea or chest pain if associated with PE.
Signs:
-Marked unilateral edema of the affected limb
-Dilated superficial collateral veins
-Tenderness to palpation
-Decreased or absent distal pulses (suggesting arterial compromise secondary to venous outflow obstruction)
-Signs of shock if massive PE is present.
Diagnostic Criteria:
-Diagnosis is suspected clinically in patients with a history of May-Thurner syndrome and iliac vein stenting who present with acute DVT symptoms
-Confirmation relies on imaging demonstrating stent occlusion
-There are no specific formal diagnostic criteria, but a high index of suspicion combined with imaging is key.

Diagnostic Approach

History Taking:
-Detailed history of previous DVT, May-Thurner syndrome diagnosis, prior venous interventions (stenting)
-Duration and progression of current symptoms
-Current antithrombotic medications and compliance
-History of hypercoagulable states
-Presence of cardiovascular risk factors
-Recent immobility or trauma.
Physical Examination:
-Comprehensive lower extremity examination: assess for edema, skin changes (erythema, cyanosis, blistering), temperature, sensation, and motor function
-Palpate for tenderness and assess peripheral pulses
-Perform a thorough cardiovascular and respiratory examination to rule out PE.
Investigations:
-Lower extremity venous Doppler ultrasound: initial modality to assess for DVT and patency of superficial and deep veins, though may be limited in deep pelvic veins
-CT venography: gold standard for visualizing iliac veins, stent patency, thrombus burden, and surrounding anatomy
-MR venography: alternative to CT venography, especially useful for assessing soft tissues
-Angiography: can be diagnostic and therapeutic, allowing for immediate intervention if thrombolysis or angioplasty is planned
-Baseline laboratory tests: complete blood count (CBC), coagulation profile (PT/INR, aPTT), renal function tests (creatinine, BUN), electrolytes, D-dimer (may be elevated but not specific for stent thrombosis).
Differential Diagnosis:
-Acute deep vein thrombosis in the absence of stenting
-Iliac vein compression due to external factors (e.g., tumor, retroperitoneal fibrosis)
-Popliteal or femoral venous thrombosis
-Acute arterial occlusion
-Cellulitis
-Lymphedema
-Lymphocele or hematoma compressing the vein.

Management

Initial Management:
-Immediate anticoagulation with unfractionated heparin (UFH) or low molecular weight heparin (LMWH) to prevent further thrombus propagation and facilitate thrombolysis
-Hemodynamic stabilization if patient is in shock
-Pain management.
Medical Management:
-Systemic thrombolysis: Intravenous infusion of fibrinolytic agents (e.g., alteplase, urokinase) may be considered, but is often less effective for extensive or chronic thrombus within a stent compared to catheter-directed thrombolysis
-Anticoagulation: Long-term anticoagulation (e.g., warfarin, direct oral anticoagulants - DOACs) is essential after successful revascularization.
Surgical Management:
-Catheter-directed thrombolysis (CDT): Infusion of thrombolytic agents directly into the thrombus via a catheter
-Mechanical thrombectomy: Use of devices to physically remove thrombus (e.g., AngioJet)
-Pharmacomechanical thrombolysis: Combination of CDT and mechanical thrombectomy
-Surgical thrombectomy: Open surgical removal of thrombus, rarely performed for isolated stent thrombosis but may be considered in conjunction with other interventions or if endovascular approaches fail
-Stent revision or replacement: If the stent is damaged or inadequate, it may require angioplasty, balloon angioplasty, or stent revision/replacement
-IVC filter placement: May be considered in patients with PE or high risk for PE, but should be carefully weighed against increased risk of recurrent thrombosis if filter is placed distal to patent venous segment.
Supportive Care:
-Close monitoring of vital signs, limb perfusion, and urine output
-Elevation of the affected limb
-Graduated compression stockings post-reperfusion to manage post-thrombotic syndrome
-Pain control
-Physical therapy and early mobilization as tolerated.

Complications

Early Complications:
-Re-thrombosis
-Bleeding (systemic or at access sites)
-Pulmonary embolism
-Distal embolization
-Vessel dissection or perforation during intervention
-Compartment syndrome
-Venous gangrene.
Late Complications:
-Post-thrombotic syndrome (chronic leg swelling, pain, hyperpigmentation, venous ulcers)
-Chronic venous insufficiency
-Recurrent venous thrombosis
-Stent restenosis or occlusion due to intimal hyperplasia.
Prevention Strategies:
-Strict adherence to optimal antithrombotic therapy post-stenting
-Thorough pre-procedural assessment for hypercoagulable states
-Careful stent selection and deployment to ensure adequate apposition and full coverage of the compressed segment
-Follow-up imaging to monitor stent patency
-Patient education on compliance with medications and recognition of early symptoms of recurrence.

Prognosis

Factors Affecting Prognosis:
-Timeliness of diagnosis and intervention
-Extent and duration of thrombosis
-Success of revascularization
-Underlying cause of May-Thurner syndrome
-Presence of comorbidities and hypercoagulable states
-Adequacy of long-term anticoagulation.
Outcomes:
-With prompt and effective surgical rescue, limb salvage and restoration of venous flow are achievable in most cases
-However, many patients develop some degree of post-thrombotic syndrome
-Long-term patency rates of revised or redeployed stents vary
-Complete resolution of symptoms is not always achieved, and chronic venous insufficiency is common.
Follow Up:
-Regular follow-up is essential, including clinical assessment and serial venous ultrasounds or other imaging modalities to monitor stent patency, assess for recurrent thrombosis, and manage post-thrombotic syndrome
-Patients require lifelong anticoagulation in many instances and need to be educated about symptom recurrence and lifestyle modifications.

Key Points

Exam Focus:
-Recognize May-Thurner stent thrombosis as an emergency requiring urgent intervention
-Understand the role of CT venography in diagnosis
-Key treatment modalities include pharmacomechanical thrombolysis and stent revision
-Differentiate from simple DVT
-Emphasize long-term anticoagulation and post-thrombotic syndrome management.
Clinical Pearls:
-A sudden increase in leg edema in a patient with prior iliac vein stenting should raise suspicion for stent thrombosis
-Do not underestimate the risk of PE
-Always consider the underlying May-Thurner anatomy and how it contributed to the initial problem and potential for recurrence.
Common Mistakes:
-Delaying intervention due to diagnostic uncertainty
-Inadequate anticoagulation post-intervention
-Failing to consider distal embolization or PE
-Not adequately assessing for underlying hypercoagulable states
-Insufficient follow-up of stent patency and management of chronic venous insufficiency.