Overview

Definition:
-Necrotizing enterocolitis (NEC) is a serious gastrointestinal emergency in neonates characterized by inflammation and necrosis of the intestinal wall
-Laparotomy is indicated for suspected or confirmed intestinal perforation, intractable sepsis, or portal venous gas
-Stoma creation, typically an ileostomy or colostomy, is often a necessary component of surgical management to divert fecal stream and allow bowel rest.
Epidemiology:
-NEC primarily affects premature infants, with incidence increasing with decreasing gestational age and birth weight
-Overall incidence ranges from 1-8% in NICU admissions, with surgical NEC occurring in about 10-30% of NEC cases
-Mortality rates for surgical NEC can be as high as 30-50%.
Clinical Significance:
-NEC represents a critical surgical emergency in neonates, demanding prompt diagnosis and intervention
-Understanding the indications for laparotomy, surgical techniques, and post-operative stoma care is vital for surgical residents preparing for DNB and NEET SS examinations, as well as for managing critically ill infants and improving outcomes.

Clinical Presentation

Symptoms:
-Abdominal distension
-Bloody stools
-Vomiting (bilious or non-bilious)
-Lethargy and irritability
-Apnea and bradycardia
-Poor feeding tolerance
-Abdominal tenderness and erythema.
Signs:
-Vital sign instability (hypotension, hypothermia, tachycardia)
-Palpable abdominal mass or rigidity
-Pneumoperitoneum on imaging
-Dilated bowel loops
-Portal venous gas on imaging
-Ascites.
Diagnostic Criteria:
-Modified Bell staging criteria are commonly used: Stage I (suspected NEC) - vague symptoms
-Stage II (definite NEC) - intestinal symptoms with focal findings
-Stage III (advanced NEC) - intestinal perforation or systemic instability
-Surgical intervention is typically reserved for Stage IIB and Stage III disease.

Diagnostic Approach

History Taking:
-Gestational age
-Birth weight
-Feeding history (prematurity, breast milk vs
-formula)
-Previous episodes of NEC or abdominal surgery
-Use of antenatal steroids
-Presence of congenital anomalies.
Physical Examination:
-Thorough abdominal examination focusing on distension, tenderness, erythema, masses, and signs of peritonitis (rigidity, guarding)
-Assess for signs of systemic compromise (respiratory distress, cardiovascular instability).
Investigations:
-Abdominal X-ray (supine and cross-table lateral views): Dilated bowel loops, intramural gas (pneumatosis intestinalis), portal venous gas, free air (pneumoperitoneum)
-Complete blood count (CBC): Leukocytosis or leukopenia, thrombocytopenia
-Electrolytes, blood gas analysis: Metabolic acidosis
-Blood cultures: Sepsis workup
-Ultrasound: Can detect free air and assess bowel wall thickness.
Differential Diagnosis:
-Intestinal obstruction (malrotation, atresia)
-Sepsis
-Colitis
-Hirschsprung disease
-Intussusception
-Congenital abdominal anomalies.

Surgical Management

Indications:
-Confirmed intestinal perforation (pneumoperitoneum on imaging)
-Intractable abdominal distension and tenderness refractory to medical management
-Clinical deterioration despite maximal medical therapy
-Portal venous gas with systemic instability
-Fixed, dilated bowel loop on imaging suggesting ischemia or perforation.
Procedure Steps:
-The goal is to resect necrotic or perforated bowel and, if necessary, create a stoma
-A midline or paramedian laparotomy is performed
-The extent of resection is determined by the viability of the bowel
-minimal resection of non-viable bowel is preferred initially
-If resection involves a significant portion of the small bowel or the colon, a stoma (ileostomy or colostomy) is typically created
-The stoma can be end or loop, depending on the bowel ends and the planned reconstruction
-If diffuse NEC is present without a clear perforation, but with severe intestinal compromise, a "second look" laparotomy may be planned.
Stoma Considerations:
-Ileostomy is more common in NEC due to the involvement of the ileocecal region
-The stoma should be well-constructed, with adequate length and caliber
-Parental education on stoma care is crucial
-Stoma sites should be carefully selected to avoid pressure points and facilitate appliance adherence.
Intestinal Resection:
-Resection of necrotic or perforated segments
-Preservation of as much viable bowel as possible
-Ligation of mesenteric vessels to control bleeding
-Primary anastomosis is rarely performed in the acute setting of NEC due to high risk of dehiscence.

Postoperative Care

Supportive Care:
-Intensive care unit (ICU) monitoring
-Mechanical ventilation
-Fluid and electrolyte management
-Blood product support
-Aggressive antibiotic therapy
-Nutritional support (parenteral nutrition initially).
Stoma Care:
-Regular stoma output monitoring
-Skin barrier protection
-Adequate hydration and electrolyte replacement
-Management of potential stoma complications (retraction, prolapse, stenosis).
Pain Management:
-Adequate analgesia to ensure comfort and facilitate recovery
-Opioids are often required initially, transitioned to non-opioid analgesics as tolerated.
Monitoring For Complications: Close observation for signs of sepsis, wound infection, intra-abdominal abscess, and further bowel compromise.

Complications

Early Complications:
-Sepsis
-Wound dehiscence
-Intra-abdominal abscess
-Further bowel necrosis
-Stoma complications (necrosis, retraction, prolapse)
-Short bowel syndrome.
Late Complications:
-Stricture formation at the anastomosis site (if primary anastomosis attempted later) or stoma site
-Adhesions leading to bowel obstruction
-Failure to thrive
-Malabsorption syndromes
-Cholestasis associated with long-term parenteral nutrition.
Prevention Strategies:
-Early recognition and medical management of NEC
-Timely surgical intervention when indicated
-Careful surgical technique to minimize bowel resection and preserve length
-Meticulous stoma construction and post-operative stoma care
-Prompt initiation of parenteral nutrition.

Prognosis

Factors Affecting Prognosis:
-Gestational age and birth weight
-Extent of bowel involved
-Presence of perforation and associated sepsis
-Need for extensive bowel resection (leading to short bowel syndrome)
-Post-operative complications.
Outcomes:
-Survival rates vary significantly based on the severity of NEC and extent of surgery, ranging from 50-80% for surgically treated infants
-Infants surviving NEC often face long-term gastrointestinal issues, requiring multidisciplinary management.
Follow Up:
-Regular growth monitoring
-Nutritional assessment
-Gastroenterology follow-up for malabsorption or feeding issues
-Surgical follow-up for stoma reversal (if planned) or management of adhesions
-Developmental assessments.

Key Points

Exam Focus:
-Indications for emergent laparotomy in NEC are clear: pneumoperitoneum, severe clinical deterioration, or fixed dilated loop
-Stoma creation is essential for fecal diversion and bowel rest
-Differentiate medical vs
-surgical NEC
-Bell staging criteria are high-yield.
Clinical Pearls:
-When in doubt about bowel viability, err on the side of caution and resect only frankly necrotic bowel, planning a "second look" if necessary
-Optimal stoma siting is critical for infant well-being and ease of care
-Early parenteral nutrition is key for intestinal rest and healing.
Common Mistakes:
-Delaying surgical intervention when indicated
-Resecting too much bowel unnecessarily
-Inadequate stoma construction or post-operative stoma care
-Underestimating the risk of sepsis or intra-abdominal abscess.