Overview

Definition:
-Orchidopexy is a surgical procedure to bring an undescended testis (cryptorchidism) into its normal scrotal position
-Undescended testis refers to a testis that has not descended into the scrotum by the age of 3-6 months
-It is one of the most common congenital anomalies of the male genitourinary tract.
Epidemiology:
-The incidence of undescended testis is approximately 3-5% in full-term neonates and up to 30% in premature infants
-It is more common on the right side and often unilateral, though bilateral involvement occurs in about 10-20% of cases
-Among infertile men, a significant proportion have a history of undescended testis.
Clinical Significance:
-Undescended testis is clinically significant due to increased risk of infertility, testicular torsion, trauma, and malignancy (testicular cancer)
-Early diagnosis and surgical correction are crucial to improve fertility potential, reduce the risk of torsion, and facilitate regular surveillance for malignancy.

Clinical Presentation

Symptoms:
-Absence of one or both testes in the scrotum on routine physical examination
-Parents may report a history of an absent or retractile testis
-Other symptoms are generally absent unless complications like torsion or infection occur
-Later, patients may present with infertility.
Signs:
-A palpable but undescended testis may be felt in the inguinal canal, suprapubic region, or abdomen
-The scrotum may appear underdeveloped or absent on the affected side
-Absence of a palpable testis in the scrotum requires thorough examination of the groin and abdomen.
Diagnostic Criteria:
-The diagnosis is primarily clinical, based on the physical examination finding of a testis not present in the scrotum by 6 months of corrected gestational age
-Imaging is usually reserved for non-palpable testes to localize them within the abdomen.

Diagnostic Approach

History Taking:
-Detailed birth history including gestational age, any antenatal abnormalities, and family history of cryptorchidism or genitourinary anomalies
-History of retractile testis and any previous medical interventions should be noted
-In older boys, inquire about symptoms of pain, swelling, or signs of puberty.
Physical Examination:
-A systematic examination of the external genitalia in a warm environment is essential
-Palpate the scrotum and inguinal regions carefully
-For palpable testes, attempt to guide them into the scrotum
-For non-palpable testes, examine the lower abdomen and perineum
-Assess for other congenital anomalies.
Investigations:
-For palpable undescended testes, no further investigations are usually required prior to surgery
-For non-palpable testes, ultrasound may identify testes in the inguinal canal or abdomen, but accuracy is operator-dependent
-MRI can be useful but is often reserved for complex cases
-Hormonal assays (e.g., FSH, LH, testosterone) are not diagnostic of undescended testis but may be considered in cases of bilateral non-palpable testes to assess testicular function and differentiate from anorchia.
Differential Diagnosis:
-Retractile testis (testis within the scrotum but can be pulled up into the inguinal canal due to cremasteric reflex, which is normal)
-Ascended testis (testis that was previously descended but has moved upwards)
-Absent testis (anorchia) due to testicular regression syndrome or congenital absence
-Swollen lymph nodes or lipoma in the inguinal region can mimic a palpable undescended testis.

Management

Initial Management:
-Referral to a pediatric surgeon or urologist for evaluation and management
-Timing of intervention is crucial
-surgical correction is generally recommended between 6 to 12 months of age to optimize fertility and reduce risks.
Medical Management:
-Hormonal therapy (e.g., human chorionic gonadotropin - hCG) can induce testicular descent in some cases (approximately 20-30% success rate), particularly for palpable testes high in the inguinal canal
-However, it is not a substitute for surgery in most cases and its efficacy is debated
-The typical regimen involves intramuscular injections of hCG (e.g., 250 IU for infants <1 year, 500 IU for 1-5 years, 1000 IU for >5 years) given three times a week for several weeks.
Surgical Management:
-Orchidopexy is the definitive treatment
-For palpable testes, an inguinal incision is made to identify and mobilize the testis, followed by fixation into a created scrotal pouch
-For non-palpable testes, laparoscopy is often used to locate the testis
-if found, it can be mobilized and brought down into the scrotum via an inguinal or scrotal incision
-If the testis is non-viable or atrophic intra-abdominally, it may be removed (orchiectomy)
-Techniques include the tension-free fixation of the testis to the dartos pouch within the scrotum, often using sutures.
Supportive Care:
-Postoperative care includes pain management, wound care, and monitoring for signs of infection or hematoma
-Follow-up appointments are essential to assess scrotal position, monitor for complications, and evaluate testicular growth and function
-Patients require lifelong surveillance for testicular cancer.

Complications

Early Complications:
-Bleeding and hematoma formation in the scrotum or inguinal region
-Wound infection
-Injury to the vas deferens or testicular vessels
-Testicular atrophy or necrosis due to compromised blood supply during mobilization
-Persistent swelling.
Late Complications:
-Recurrence of undescended testis (testis retracts or descends again)
-Infertility (risk is increased even after successful orchidopexy, especially in bilateral cases)
-Testicular torsion
-Development of testicular cancer (risk remains higher than general population)
-Chronic pain
-Cosmetic dissatisfaction.
Prevention Strategies:
-Meticulous surgical technique by experienced surgeons
-Careful dissection to preserve testicular vasculature
-Adequate mobilization of the spermatic cord
-Secure fixation of the testis in the scrotum without excessive tension
-Careful postoperative wound care
-Regular surveillance for late complications.

Prognosis

Factors Affecting Prognosis:
-The degree of testicular maldescent (intra-abdominal testes have poorer outcomes), presence of associated anomalies, age at surgery, and fertility status of the contralateral testis
-Bilateral undescended testes and intra-abdominal testes have a worse prognosis for fertility.
Outcomes:
-Successful orchidopexy leads to the testis residing in the scrotum, reducing the risk of torsion and facilitating cancer surveillance
-Fertility outcomes are variable
-early surgical correction (before 1-2 years) is associated with better preservation of spermatogenesis
-The risk of testicular cancer is reduced but not eliminated, necessitating lifelong follow-up.
Follow Up:
-Long-term follow-up is essential
-This includes regular physical examinations to assess testicular position, size, and consistency, typically annually until adulthood
-Semen analysis may be considered in adolescence if fertility is a concern
-Patients and families should be educated about the signs and symptoms of testicular torsion and cancer.

Key Points

Exam Focus:
-Understand the timing of diagnosis and surgical intervention for undescended testis (6-12 months)
-Differentiate between palpable and non-palpable testes
-Know the indications for laparoscopic versus open orchidopexy
-Recall the hormonal therapy regimens and success rates
-Recognize the long-term risks of infertility, torsion, and malignancy.
Clinical Pearls:
-Always examine the scrotum and inguinal region in a warm environment
-A retractile testis is normal and does not require orchidopexy
-Consider the possibility of bilateral undescended testes if one is absent
-Early intervention is key for optimizing fertility
-Patients with a history of cryptorchidism are at increased risk for testicular cancer and require lifelong surveillance.
Common Mistakes:
-Delaying surgery beyond 18-24 months of age
-Relying solely on imaging for diagnosis of non-palpable testes without surgical exploration
-Inadequate mobilization of the spermatic cord leading to tension on the testis
-Failing to counsel patients and parents on long-term risks and follow-up requirements
-Misdiagnosing a retractile testis as a true undescended testis.