Overview

Definition:
-Perianal Crohn's disease refers to the manifestation of Crohn's disease in the perianal region, often presenting as fistulas, abscesses, skin tags, and fissures
-Seton placement is a surgical technique used for drainage and/or partial closure of complex perianal fistulas, aiming to manage sepsis, preserve continence, and facilitate healing while addressing the underlying inflammatory process.
Epidemiology:
-Perianal involvement occurs in approximately 25-35% of patients with Crohn's disease
-Complex perianal fistulas, those that are high, multiple, or associated with abscesses, often require surgical intervention, including seton placement
-It is more common in younger adults and can significantly impact quality of life.
Clinical Significance:
-Uncontrolled perianal Crohn's disease can lead to significant morbidity, including chronic pain, recurrent sepsis, incontinence, and a high risk of anal strictures or loss of sphincter function
-Effective seton strategies are crucial for managing these complex cases, preventing complications, and optimizing patient outcomes in surgical practice.

Clinical Presentation

Symptoms:
-Painful perianal mass or swelling
-Anal discharge, which may be purulent, bloody, or feculent
-Perianal itching or irritation
-Fecal incontinence or urgency
-Fever and malaise, indicative of abscess
-Palpable perianal fistula tracts.
Signs:
-Visible external fistula openings
-Erythema and tenderness around the anus
-Induration suggestive of abscess or thickened fistula tract
-Perianal skin tags or fissures
-Proctitis or mucosal inflammation on digital rectal examination or anoscopy
-Palpable internal and external sphincter involvement in some cases.
Diagnostic Criteria:
-Diagnosis is primarily clinical, supported by imaging
-Symptoms suggestive of perianal disease in a patient with known or suspected Crohn's disease
-Physical examination revealing perianal abnormalities
-Confirmation of fistula tract and abscess by imaging modalities like MRI pelvis or endoanal ultrasound is essential for surgical planning.

Diagnostic Approach

History Taking:
-Detailed history of bowel habits, stool consistency, and any leakage or pain
-Previous perianal procedures or infections
-History of Crohn's disease diagnosis, location of disease, and current medical management
-Assessment of nutritional status and any systemic symptoms of active Crohn's disease
-Inquiry about continence and quality of life.
Physical Examination:
-Gentle perianal inspection and palpation
-Digital rectal examination to assess sphincter tone, internal openings, and intersphincteric plane involvement
-Careful assessment for abscesses, induration, and external fistula openings
-Anoscopy to visualize internal openings and mucosal disease
-Avoid aggressive examination that may precipitate sepsis.
Investigations:
-Magnetic Resonance Imaging (MRI) of the pelvis with fistula protocol is the gold standard for characterizing fistula anatomy, including internal and external openings, tract course, presence of sepsis, and extent of sphincter involvement
-Endoluminal Ultrasound (EUS) can be useful for detailing the relation to the sphincter complex
-Laboratory tests include CBC (leukocytosis may indicate sepsis), ESR, CRP (markers of inflammation), and stool studies to rule out infection
-Colonoscopy may be used to assess the extent of intestinal Crohn's disease.
Differential Diagnosis:
-Simple anal fissure
-Perianal abscess of non-Crohn's etiology
-Hidradenitis suppurativa
-Pilonidal sinus disease
-Sexually transmitted infections causing perianal lesions
-Tuberculosis of the perianal region
-Lymphogranuloma venereum.

Management

Initial Management:
-Management of active sepsis is paramount
-This includes prompt drainage of perianal abscesses
-Medical management with antibiotics (e.g., ciprofloxacin and metronidazole) for suspected or confirmed infection
-Pain control with appropriate analgesics
-Nutritional support.
Medical Management:
-While not curative for fistulas, medical therapy aims to control underlying inflammation and may promote healing
-Immunomodulators (azathioprine, 6-mercaptopurine) and biologics (infliximab, adalimumab) are cornerstone treatments for Crohn's disease, including perianal manifestations
-Antibiotics are used for infection control.
Surgical Management:
-Surgical goal is to control sepsis, preserve sphincter function, and promote healing
-Seton placement is a key strategy for complex perianal fistulas
-Types of setons include: Loose setons (draining, allowing gradual closure), cutting setons (slowly cutting through the sphincter), and videolaparoscopic-assisted anal fistula treatment (VAAFT) combined with seton drainage
-Indications for seton placement include complex, high, multiple, or recurrent anal fistulas, especially those involving a significant portion of the sphincter complex or associated with abscesses
-The choice of seton depends on fistula complexity, risk of incontinence, and surgeon preference.
Supportive Care:
-Wound care and hygiene are critical
-Regular sitz baths can help with comfort and cleanliness
-Nutritional optimization with adequate protein and micronutrients
-Psychological support to address the impact of chronic illness and body image concerns
-Multidisciplinary team approach involving gastroenterologists, surgeons, radiologists, and stoma nurses.

Seton Strategies

Indications For Seton:
-Transsphincteric or extrasphincteric fistulas involving >30-50% of the sphincter complex
-Recurrent fistulas after previous treatment
-Abscesses requiring drainage in the setting of significant sphincter involvement
-To avoid immediate fistulotomy in patients with high risk of incontinence
-To promote granulation and partial closure of draining fistulas.
Types Of Setons:
-Draining setons (e.g., silk, latex bands) used to keep fistula tracts open and drain pus, allowing healing from the base upwards
-Cutting setons (e.g., heavy silk, braided nylon) used to slowly divide the sphincter muscle over time, reducing incontinence risk
-Plug or biologics used in conjunction with seton or as an alternative for specific fistula types.
Placement Techniques:
-Performed under anesthesia
-Identify internal and external openings
-Gently probe the fistula tract
-Pass a suitable seton material through the tract
-Tie the ends securely but not too tightly to allow drainage
-Draining setons are often loosely tied, while cutting setons are tightened periodically
-Adjunctive procedures like curettage of the tract may be performed
-MRI guidance can be helpful for complex anatomy.
Post Seton Management:
-Regular follow-up to monitor for drainage, pain, and signs of infection
-Gentle cleaning of the perianal area
-Periodic tightening of cutting setons if indicated
-Oral antibiotics if infection develops
-Pain management
-Patient education on wound care and signs of complications
-Gradual removal of draining setons as tracts close or when surgical intervention for definitive treatment is planned.

Complications

Early Complications:
-Pain at the seton site
-Bleeding
-Infection or abscess formation around the seton
-Migration or extrusion of the seton
-Urosepsis if the tract is near the urinary system.
Late Complications:
-Incontinence (temporary or permanent), especially with cutting setons
-Rectovaginal or urethrocutaneous fistula formation
-Anal stricture
-Recurrence of fistula
-Failure of seton to adequately drain or promote healing.
Prevention Strategies:
-Careful patient selection and accurate fistula mapping with MRI
-Judicious use of cutting setons in patients with risk factors for incontinence
-Proper placement and secure fixation of the seton
-Aggressive management of any early signs of infection or abscess
-Adequate pain control
-Patient education on wound care.

Prognosis

Factors Affecting Prognosis:
-Extent and complexity of the fistula
-Degree of sphincter involvement
-Presence and control of active Crohn's disease elsewhere
-Response to medical therapy
-Adherence to wound care and follow-up
-Surgeon's experience.
Outcomes:
-Seton therapy is primarily a temporizing or palliative measure to control sepsis and preserve function
-Complete healing may occur in some patients, particularly with draining setons
-For many, it allows for better control while awaiting definitive surgery or as part of a long-term management strategy
-Rates of healing vary widely, with some studies reporting up to 50-70% healing with appropriate medical and surgical management, including setons.
Follow Up:
-Long-term and regular follow-up is essential
-This includes clinical assessment, imaging as needed (e.g., repeat MRI if symptoms recur), and monitoring for complications
-Patients require ongoing management of their underlying Crohn's disease
-Transition to definitive surgical management (e.g., advancement flap, LIFT procedure, or proctectomy in refractory cases) may be considered after seton treatment.

Key Points

Exam Focus:
-Understand the indications for seton placement in perianal Crohn's disease
-Differentiate between draining and cutting setons and their respective roles
-Recognize the importance of MRI in fistula characterization
-Know the complications associated with seton therapy, especially incontinence
-Recall the multimodal approach to perianal Crohn's disease management.
Clinical Pearls:
-Always consider sepsis first and drain abscesses
-MRI is indispensable for surgical planning
-When in doubt about sphincter involvement, err on the side of caution with seton placement over immediate fistulotomy
-Involve a multidisciplinary team
-Educate patients thoroughly about the process and expectations.
Common Mistakes:
-Performing aggressive digital rectal exams that can worsen sepsis
-Undertaking blind fistulotomy in high transsphincteric fistulas without adequate imaging
-Neglecting underlying Crohn's disease activity
-Inadequate patient follow-up and wound care
-Premature removal of setons before tracts are sufficiently healed.