Definition/General

Introduction:
-Ductal carcinoma in situ (DCIS) is a non-invasive breast cancer where malignant epithelial cells are confined to the breast ducts, without invasion of the basement membrane
-It is considered a precursor lesion to invasive ductal carcinoma.
Origin:
-DCIS arises from the terminal duct-lobular unit (TDLU)
-It is a clonal proliferation of malignant cells that fill and distend the ducts.
Classification:
-DCIS is classified based on architectural patterns (e.g., comedo, cribriform, solid, papillary, micropapillary) and nuclear grade (low, intermediate, high)
-The presence of necrosis is also an important feature.
Epidemiology:
-The incidence of DCIS has increased dramatically with the widespread use of screening mammography
-It now accounts for about 20% of all breast cancer diagnoses
-It is most common in postmenopausal women.

Clinical Features

Presentation:
-Most cases of DCIS are asymptomatic and are detected by mammography as calcifications
-Less commonly, it can present as a palpable mass or nipple discharge.
Symptoms:
-Usually asymptomatic
-When symptoms occur, they can include a breast lump, nipple discharge (often bloody), or Paget disease of the nipple.
Risk Factors: The risk factors are similar to those for invasive breast cancer, including age, family history, and hormonal factors.
Screening:
-Mammography is the primary method of detection
-The characteristic finding is pleomorphic microcalcifications in a linear or branching distribution.

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Gross Description

Appearance:
-DCIS is often not grossly visible
-When it is, it may appear as a poorly defined, firm, white area
-In comedo-type DCIS, the cut surface may show ducts filled with cheesy, necrotic material.
Characteristics: The involved area may feel slightly firmer than the surrounding tissue.
Size Location:
-The extent of DCIS can be variable, from a small focus to widespread involvement of a breast quadrant.
Multifocality: DCIS can be multifocal and multicentric.

Microscopic Description

Histological Features:
-The ducts are filled with a malignant epithelial proliferation
-The cells are confined by the basement membrane, and a myoepithelial cell layer is preserved
-The key features are the architectural pattern and nuclear grade.
Cellular Characteristics:
-The tumor cells show varying degrees of atypia, from bland, monotonous cells in low-grade DCIS to highly pleomorphic cells with prominent nucleoli in high-grade DCIS
-Mitotic activity is variable.
Architectural Patterns:
-Comedo: solid sheets of high-grade cells with central necrosis
-Cribriform: sieve-like spaces
-Solid: ducts completely filled with tumor cells
-Papillary: fibrovascular cores
-Micropapillary: tufts of cells without fibrovascular cores.
Grading Criteria:
-Grading is based on nuclear pleomorphism and the presence of necrosis
-Low grade: monotonous nuclei, rare mitoses, no necrosis
-High grade: pleomorphic nuclei, frequent mitoses, comedonecrosis
-Intermediate grade: features in between.

Immunohistochemistry

Positive Markers:
-The tumor cells are positive for cytokeratins (e.g., CK7)
-Most DCIS is ER-positive
-HER2 is overexpressed in a subset of cases, particularly high-grade DCIS.
Negative Markers:
-The myoepithelial cell layer, which is preserved, is positive for myoepithelial markers like p63 and calponin
-This is a key feature to distinguish DCIS from invasive carcinoma.
Diagnostic Utility:
-IHC for myoepithelial markers is crucial to differentiate DCIS from invasive carcinoma
-ER, PR, and HER2 status are important for predicting the risk of recurrence and for guiding therapy.
Molecular Subtypes:
-DCIS can be classified into molecular subtypes similar to invasive cancer, with the luminal type being the most common.

Molecular/Genetic

Genetic Mutations:
-The genetic alterations in DCIS are similar to those in invasive ductal carcinoma, including loss of heterozygosity at several loci and mutations in genes like PIK3CA and TP53.
Molecular Markers: The molecular profile of DCIS is often similar to that of the invasive carcinoma that it may progress to.
Prognostic Significance:
-The main risk associated with DCIS is the potential for progression to invasive carcinoma
-The risk of recurrence after treatment depends on the grade, size, and margin status.
Therapeutic Targets:
-Treatment is aimed at preventing progression to invasive cancer and includes surgery (lumpectomy or mastectomy) and often radiation
-Endocrine therapy (e.g., tamoxifen) is used for ER-positive DCIS.

Differential Diagnosis

Similar Entities:
-Atypical ductal hyperplasia (ADH)
-Usual ductal hyperplasia (UDH)
-Invasive ductal carcinoma.
Distinguishing Features:
-ADH is distinguished from low-grade DCIS by its size (<2 mm) and extent (involving <2 ducts)
-UDH has a mixed cell population and irregular slit-like spaces
-Invasive carcinoma lacks a myoepithelial layer around the tumor nests.
Diagnostic Challenges: The distinction between ADH and low-grade DCIS can be subjective and is a common reason for consultation in breast pathology.
Rare Variants: DCIS can show various special features, such as apocrine, clear cell, or signet ring cell morphology.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen Information

[specimen type], measuring [size] cm in greatest dimension

Diagnosis

[diagnosis name]

Classification

Classification: [classification system] [grade/type]

Histological Features

Shows [architectural pattern] with [nuclear features] and [mitotic activity]

Size and Extent

Size: [X] cm, extent: [local/regional/metastatic]

Margins

Margins are [involved/uninvolved] with closest margin [X] mm

Lymphovascular Invasion

Lymphovascular invasion: [present/absent]

Lymph Node Status

Lymph nodes: [X] positive out of [X] examined

Special Studies

IHC: [marker]: [result]

Molecular: [test]: [result]

[other study]: [result]

Final Diagnosis

Final diagnosis: [complete diagnosis]