Definition/General

Introduction:
-Juvenile fibroadenoma is a variant of fibroadenoma that occurs in adolescents and young women
-It is characterized by rapid growth and a more cellular stroma than a conventional fibroadenoma.
Origin: It arises from the terminal duct-lobular unit (TDLU).
Classification: It is a subtype of fibroadenoma.
Epidemiology: It is most common in African American adolescents and typically occurs between the ages of 10 and 20.

Clinical Features

Presentation: Presents as a large, rapidly growing, painless, mobile mass.
Symptoms: A rapidly enlarging breast lump is the most common symptom.
Risk Factors: There are no well-established risk factors.
Screening: Ultrasound shows a well-defined, hypoechoic mass.

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Gross Description

Appearance:
-A large, well-circumscribed, encapsulated, gray-white mass.
Characteristics: The cut surface is firm and whorled.
Size Location:
-Can be very large, sometimes replacing most of the breast tissue.
Multifocality: Can be multiple.

Microscopic Description

Histological Features:
-The lesion is a biphasic tumor with a more cellular stroma and a more florid epithelial proliferation than a conventional fibroadenoma
-The glands are often elongated and compressed.
Cellular Characteristics:
-The stromal cells are plump and cellular, but lack significant atypia and mitotic activity
-The epithelial cells can show hyperplasia.
Architectural Patterns: A pericanalicular pattern is more common than an intracanalicular pattern.
Grading Criteria: This is a benign lesion.

Immunohistochemistry

Positive Markers: The IHC profile is similar to that of a conventional fibroadenoma.
Negative Markers: Not typically required for diagnosis.
Diagnostic Utility: IHC is not usually necessary for diagnosis.
Molecular Subtypes: Molecular subtyping is not relevant for this benign condition.

Molecular/Genetic

Genetic Mutations: Not well characterized.
Molecular Markers: No specific molecular markers are routinely used for diagnosis.
Prognostic Significance:
-This is a benign lesion with an excellent prognosis
-Recurrence is rare after complete excision.
Therapeutic Targets: Treatment is surgical excision.

Differential Diagnosis

Similar Entities:
-Benign phyllodes tumor
-Conventional fibroadenoma.
Distinguishing Features:
-Benign phyllodes tumors have a more cellular stroma, often with a leaf-like architecture
-The distinction from a cellular fibroadenoma can be difficult.
Diagnostic Challenges: The main challenge is distinguishing a juvenile fibroadenoma from a benign phyllodes tumor, especially on a core needle biopsy.
Rare Variants: There are no specific rare variants.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen Information

[specimen type], measuring [size] cm in greatest dimension

Diagnosis

[diagnosis name]

Classification

Classification: [classification system] [grade/type]

Histological Features

Shows [architectural pattern] with [nuclear features] and [mitotic activity]

Size and Extent

Size: [X] cm, extent: [local/regional/metastatic]

Margins

Margins are [involved/uninvolved] with closest margin [X] mm

Lymphovascular Invasion

Lymphovascular invasion: [present/absent]

Lymph Node Status

Lymph nodes: [X] positive out of [X] examined

Special Studies

IHC: [marker]: [result]

Molecular: [test]: [result]

[other study]: [result]

Final Diagnosis

Final diagnosis: [complete diagnosis]