Definition/General

Introduction:
-Sclerosing adenosis is a benign proliferative breast lesion characterized by a proliferation of glandular and myoepithelial cells, associated with stromal sclerosis
-It can mimic invasive carcinoma both clinically and mammographically.
Origin:
-It arises from the terminal duct-lobular unit (TDLU)
-It is a type of adenosis, which is a general term for an increase in the number of glands.
Classification:
-Sclerosing adenosis is classified as a benign proliferative breast lesion without atypia
-It is a component of fibrocystic changes.
Epidemiology:
-It is a common finding in breast biopsies, especially in the perimenopausal age group.

Clinical Features

Presentation: It can present as a palpable mass or be detected on mammography as a spiculated mass or calcifications, raising suspicion for malignancy.
Symptoms: It can be associated with breast pain (mastalgia).
Risk Factors: Not applicable.
Screening: Mammographically, it can mimic invasive carcinoma, showing a spiculated mass, architectural distortion, or microcalcifications.

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Gross Description

Appearance:
-It may not have a distinct gross appearance
-When it forms a mass, it is typically a firm, rubbery, ill-defined lesion.
Characteristics: The cut surface is gray-white and fibrous.
Size Location:
-Usually small, but can form a palpable mass.
Multifocality: Can be multifocal.

Microscopic Description

Histological Features:
-The lesion is characterized by a proliferation of small, compressed glands in a dense, sclerotic stroma
-The glands are arranged in a swirling or whorled pattern
-The key feature is the preservation of the lobulocentric architecture and the presence of a myoepithelial cell layer.
Cellular Characteristics:
-The epithelial cells are bland, with small, uniform nuclei
-The myoepithelial cells are also present and can be prominent.
Architectural Patterns:
-The glands are often distorted and compressed by the sclerotic stroma, which can mimic the infiltrative pattern of invasive carcinoma.
Grading Criteria: This is a benign lesion.

Immunohistochemistry

Positive Markers:
-The myoepithelial cell layer is highlighted by myoepithelial markers such as p63, calponin, and smooth muscle actin (SMA)
-The epithelial cells are positive for cytokeratins.
Negative Markers: Not applicable.
Diagnostic Utility:
-IHC for myoepithelial markers is crucial to differentiate sclerosing adenosis from invasive carcinoma, especially tubular carcinoma
-The presence of a continuous myoepithelial layer confirms the benign nature of the lesion.
Molecular Subtypes: Not applicable.

Molecular/Genetic

Genetic Mutations: Not applicable.
Molecular Markers: No specific molecular markers are routinely used for diagnosis.
Prognostic Significance: Sclerosing adenosis is associated with a small increased risk (about 1.5-2 fold) of developing invasive breast cancer.
Therapeutic Targets:
-No specific treatment is required
-Management is focused on excluding malignancy.

Differential Diagnosis

Similar Entities:
-Invasive ductal carcinoma, especially tubular carcinoma
-Radial scar.
Distinguishing Features:
-Tubular carcinoma lacks a myoepithelial layer around the infiltrating tubules
-A radial scar has a central fibroelastotic core and entrapped glands, but the overall architecture is different.
Diagnostic Challenges:
-The main challenge is distinguishing sclerosing adenosis from invasive carcinoma on small biopsies
-The distorted glands can be very suspicious
-IHC for myoepithelial markers is essential in these cases.
Rare Variants: Not applicable.

Sample Pathology Report

Template Format

Sample Pathology Report

Complete Report: This is an example of how the final pathology report should be structured for this condition.

Specimen Information

[specimen type], measuring [size] cm in greatest dimension

Diagnosis

[diagnosis name]

Classification

Classification: [classification system] [grade/type]

Histological Features

Shows [architectural pattern] with [nuclear features] and [mitotic activity]

Size and Extent

Size: [X] cm, extent: [local/regional/metastatic]

Margins

Margins are [involved/uninvolved] with closest margin [X] mm

Lymphovascular Invasion

Lymphovascular invasion: [present/absent]

Lymph Node Status

Lymph nodes: [X] positive out of [X] examined

Special Studies

IHC: [marker]: [result]

Molecular: [test]: [result]

[other study]: [result]

Final Diagnosis

Final diagnosis: [complete diagnosis]